In-vitro and in-vivo consequences of mutations in the von Willebrand factor cleaving protease ADAMTS13 in thrombotic thrombocytopenic purpura.
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Pathophysiology of thrombotic thrombocytopenic purpuraProteolytic processing of von Willebrand factor by adamts13 and leukocyte proteasesThrombotic thrombocytopenic purpura: a thrombotic disorder caused by ADAMTS13 deficiencyThe kidney in thrombotic thrombocytopenic purpura.The first deletion mutation in the TSP1-6 repeat domain of ADAMTS13 in a family with inherited thrombotic thrombocytopenic purpura.Mechanisms of microvascular thrombosis in thrombotic thrombocytopenic purpura.Residual plasmatic activity of ADAMTS13 is correlated with phenotype severity in congenital thrombotic thrombocytopenic purpura.Hereditary ADAMTS 13 deficiency presenting as recurrent acute kidney injury.ADAMTS13 Secretion and Residual Activity among Patients with Congenital Thrombotic Thrombocytopenic Purpura with and without Renal Impairment.Cyclosporin A impairs the secretion and activity of ADAMTS13 (a disintegrin and metalloprotease with thrombospondin type 1 repeat).N-Glycans of ADAMTS13 modulate its secretion and von Willebrand factor cleaving activity.Inherited thrombotic thrombocytopenic purpura.
P2860
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P2860
In-vitro and in-vivo consequences of mutations in the von Willebrand factor cleaving protease ADAMTS13 in thrombotic thrombocytopenic purpura.
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2006 nî lūn-bûn
@nan
2006 թուականի Հոկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2006 թվականի հոտեմբերին հրատարակված գիտական հոդված
@hy
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
name
In-vitro and in-vivo consequen ...... otic thrombocytopenic purpura.
@ast
In-vitro and in-vivo consequen ...... otic thrombocytopenic purpura.
@en
type
label
In-vitro and in-vivo consequen ...... otic thrombocytopenic purpura.
@ast
In-vitro and in-vivo consequen ...... otic thrombocytopenic purpura.
@en
prefLabel
In-vitro and in-vivo consequen ...... otic thrombocytopenic purpura.
@ast
In-vitro and in-vivo consequen ...... otic thrombocytopenic purpura.
@en
P2093
P1476
In-vitro and in-vivo consequen ...... otic thrombocytopenic purpura.
@en
P2093
Constantino Martinez
Cristina Capoferri
Edoardo Rossi
Elena Bresin
Federica Banterla
Friedrich Scheiflinger
Giuseppe Monteferrante
International Registry of Recurrent and Familial HUS/TTP
Marina Noris
Miriam Galbusera
P304
P577
2006-10-01T00:00:00Z