Hyperfunctional C3 convertase leads to complement deposition on endothelial cells and contributes to atypical hemolytic uremic syndrome. - Wikidata - wikimedia - TriplyDB

Hyperfunctional C3 convertase leads to complement deposition on endothelial cells and contributes to atypical hemolytic uremic syndrome.

Hyperfunctional C3 convertase leads to complement deposition on endothelial cells and contributes to atypical hemolytic uremic syndrome.

http://www.wikidata.org/entity/Q33385299

about

Atypical hemolytic uremic syndrome Clinical features of anti-factor H autoantibody-associated hemolytic uremic syndrome Hemolytic uremic syndrome: new developments in pathogenesis and treatment Relative role of genetic complement abnormalities in sporadic and familial aHUS and their impact on clinical phenotype Advances and challenges in the management of complement-mediated thrombotic microangiopathies Hemolytic uremic syndrome Complement System Part II: Role in Immunity Haemolytic uraemic syndrome.Pregnancy-associated hemolytic uremic syndrome revisited in the era of complement gene mutations.Genetics and complement in atypical HUS.Advances in understanding the aetiology of atypical Haemolytic Uraemic Syndrome.New insights into postrenal transplant hemolytic uremic syndrome.Complement-mediated injury and protection of endothelium: lessons from atypical haemolytic uraemic syndrome A prevalent C3 mutation in aHUS patients causes a direct C3 convertase gain of function.STEC-HUS, atypical HUS and TTP are all diseases of complement activation.Genetics and outcome of atypical hemolytic uremic syndrome: a nationwide French series comparing children and adults.Complement genes strongly predict recurrence and graft outcome in adult renal transplant recipients with atypical hemolytic and uremic syndrome.Combined complement gene mutations in atypical hemolytic uremic syndrome influence clinical phenotype.Complement therapy in atypical haemolytic uraemic syndrome (aHUS).Macrovascular involvement in a child with atypical hemolytic uremic syndrome.Complement factor B mutations in atypical hemolytic uremic syndrome-disease-relevant or benign?A complement factor B mutation in a large kindred with atypical hemolytic uremic syndrome.Dynamics of complement activation in aHUS and how to monitor eculizumab therapy COMPLEMENTing the diagnosis of aHUS Postoperative atypical hemolytic uremic syndrome associated with complement c3 mutation.Atypical hemolytic uremic syndrome post-kidney transplantation: two case reports and review of the literature Mapping interactions between complement C3 and regulators using mutations in atypical hemolytic uremic syndrome.Diabetic ketoacidosis presenting with atypical hemolytic uremic syndrome associated with a variant of complement factor B in an adult: a case report.A Case Report and Literature Review of Eculizumab Withdrawal in Atypical Hemolytic-Uremic Syndrome HUS and atypical HUS.Complement System Part I - Molecular Mechanisms of Activation and Regulation.Antibody directs properdin-dependent activation of the complement alternative pathway in a mouse model of abdominal aortic aneurysm A Familial C3GN Secondary to Defective C3 Regulation by Complement Receptor 1 and Complement Factor H Turkish pediatric atypical hemolytic uremic syndrome registry: initial analysis of 146 patients Functional Characterization of Autoantibodies against Complement Component C3 in Patients with Lupus Nephritis.MAE4, an eLtaS monoclonal antibody, blocks Staphylococcus aureus virulence.The Genetics of Ultra-Rare Renal Disease.Update on hemolytic uremic syndrome: Diagnostic and therapeutic recommendations.Complement related kidney diseases: Recurrence after transplantation.Kidney Disease Caused by Dysregulation of the Complement Alternative Pathway: An Etiologic Approach.

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P2860

Hyperfunctional C3 convertase leads to complement deposition on endothelial cells and contributes to atypical hemolytic uremic syndrome.

http://www.wikidata.org/entity/Q33385299

description

2009 nî lūn-bûn

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2009 թուականի Յուլիսին հրատարակուած գիտական յօդուած

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2009 թվականի հուլիսին հրատարակված գիտական հոդված

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2009年の論文

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2009年論文

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2009年論文

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2009年論文

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2009年論文

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2009年論文

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2009年论文

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name

Hyperfunctional C3 convertase ...... cal hemolytic uremic syndrome.

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Hyperfunctional C3 convertase ...... cal hemolytic uremic syndrome.

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Hyperfunctional C3 convertase ...... cal hemolytic uremic syndrome.

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Hyperfunctional C3 convertase ...... cal hemolytic uremic syndrome.

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Hyperfunctional C3 convertase ...... cal hemolytic uremic syndrome.

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Chantal Loirat

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Christophe Hue

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David Ribes

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Jacques Blouin

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Lise Halbwachs-Mecarelli

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Luc Moulonguet

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Marie-Agnes Dragon-Durey

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Marie-Alice Macher

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Mathieu Cayla

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Mathieu Jablonski

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2837-2845

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Peter Mathieson

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Catherine Sautès-Fridman

Wolf Hervé Fridman

Marie-Alice Macher

Marie-Agnès Dragon-Durey

Lise Halbwachs-Mecarelli

Jordan D Dimitrov

Lubka T. Roumenina

Catherine H Regnier

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26653886

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