Reduced inhibitory effect of Mg2+ on ryanodine receptor-Ca2+ release channels in malignant hyperthermia.
about
The glutathione transferase structural family includes a nuclear chloride channel and a ryanodine receptor calcium release channel modulatorDivergent effects of the malignant hyperthermia-susceptible Arg(615)-->Cys mutation on the Ca(2+) and Mg(2+) dependence of the RyR1.Involvement of the cardiac ryanodine receptor/calcium release channel in catecholaminergic polymorphic ventricular tachycardiaDifferent Ca2+ releasing action of caffeine and depolarisation in skeletal muscle fibres of the ratArg(615)Cys substitution in pig skeletal ryanodine receptors increases activation of single channels by a segment of the skeletal DHPR II-III loopCharacteristics of irreversible ATP activation suggest that native skeletal ryanodine receptors can be phosphorylated via an endogenous CaMKIIRegulation of the calcium release channel from rabbit skeletal muscle by the nucleotides ATP, AMP, IMP and adenosineInterdomain interactions within ryanodine receptors regulate Ca2+ spark frequency in skeletal muscle.Genetics and pathogenesis of malignant hyperthermia.Differences in the regulation of RyR2 from human, sheep, and rat by Ca²⁺ and Mg²⁺ in the cytoplasm and in the lumen of the sarcoplasmic reticulum.Inactivation of Ca2+ release channels (ryanodine receptors RyR1 and RyR2) with rapid steps in [Ca2+] and voltage.Activation and inhibition of skeletal RyR channels by a part of the skeletal DHPR II-III loop: effects of DHPR Ser687 and FKBP12.Oxidation and reduction of pig skeletal muscle ryanodine receptors.Effects of cytoplasmic and luminal pH on Ca(2+) release channels from rabbit skeletal muscle.Regulation of the calcium release channel from skeletal muscle by suramin and the disulfonated stilbene derivatives DIDS, DBDS, and DNDS.Functional defects in six ryanodine receptor isoform-1 (RyR1) mutations associated with malignant hyperthermia and their impact on skeletal excitation-contraction coupling.Malignant hyperthermia and excitation-contraction coupling.The power of single channel recording and analysis: its application to ryanodine receptors in lipid bilayers.Functional and biochemical properties of ryanodine receptor type 1 channels from heterozygous R163C malignant hyperthermia-susceptible mice.Gene dose influences cellular and calcium channel dysregulation in heterozygous and homozygous T4826I-RYR1 malignant hyperthermia-susceptible muscle.Intercellular Ca(2+) waves: mechanisms and function.Nonspecific sarcolemmal cation channels are critical for the pathogenesis of malignant hyperthermia.Modulation of the local SR Ca2+ release by intracellular Mg2+ in cardiac myocytes.Calcium-induced calcium release in skeletal muscle.Ryanodine receptors: physiological function and deregulation in Alzheimer disease.Regulation of skeletal ryanodine receptors by dihydropyridine receptor II-III loop C-region peptides: relief of Mg2+ inhibition.Reduced threshold for luminal Ca2+ activation of RyR1 underlies a causal mechanism of porcine malignant hyperthermia.Voltage-dependent calcium release in human malignant hyperthermia muscle fibers.Sulfhydryl oxidation overrides Mg(2+) inhibition of calcium-induced calcium release in skeletal muscle triads.Extensive Ca2+ leak through K4750Q cardiac ryanodine receptors caused by cytosolic and luminal Ca2+ hypersensitivity.Magnesium Sensitizes Slow Vacuolar Channels to Physiological Cytosolic Calcium and Inhibits Fast Vacuolar Channels in Fava Bean Guard Cell Vacuoles.Postulated role of interdomain interaction between regions 1 and 2 within type 1 ryanodine receptor in the pathogenesis of porcine malignant hyperthermia.Mind the magnesium, in dantrolene suppression of malignant hyperthermia.Dantrolene requires Mg2+ to arrest malignant hyperthermia.Effects of a domain peptide of the ryanodine receptor on Ca2+ release in skinned skeletal muscle fibers.Caffeine sensitivity of native RyR channels from normal and malignant hyperthermic pigs: effects of a DHPR II-III loop peptide.Phospholamban phosphorylation increases the passive calcium leak from cardiac sarcoplasmic reticulum.Effects of dihydropyridine receptor II-III loop peptides on Ca(2+) release in skinned skeletal muscle fibers.
P2860
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P2860
Reduced inhibitory effect of Mg2+ on ryanodine receptor-Ca2+ release channels in malignant hyperthermia.
description
1997 nî lūn-bûn
@nan
1997 թուականի Հոկտեմբերին հրատարակուած գիտական յօդուած
@hyw
1997 թվականի հոտեմբերին հրատարակված գիտական հոդված
@hy
1997年の論文
@ja
1997年論文
@yue
1997年論文
@zh-hant
1997年論文
@zh-hk
1997年論文
@zh-mo
1997年論文
@zh-tw
1997年论文
@wuu
name
Reduced inhibitory effect of M ...... els in malignant hyperthermia.
@ast
Reduced inhibitory effect of M ...... els in malignant hyperthermia.
@en
type
label
Reduced inhibitory effect of M ...... els in malignant hyperthermia.
@ast
Reduced inhibitory effect of M ...... els in malignant hyperthermia.
@en
prefLabel
Reduced inhibitory effect of M ...... els in malignant hyperthermia.
@ast
Reduced inhibitory effect of M ...... els in malignant hyperthermia.
@en
P2093
P2860
P1433
P1476
Reduced inhibitory effect of M ...... nels in malignant hyperthermia
@en
P2093
P2860
P304
P356
10.1016/S0006-3495(97)78222-5
P407
P577
1997-10-01T00:00:00Z