A myopathy-linked tropomyosin mutation severely alters thin filament conformational changes during activation.
about
Tropomodulin capping of actin filaments in striated muscle development and physiologyPointed-end capping by tropomodulin modulates actomyosin crossbridge formation in skeletal muscle fibers.X-ray diffraction from flight muscle with a headless myosin mutation: implications for interpreting reflection patternsNemaline myopathy-related skeletal muscle α-actin (ACTA1) mutation, Asp286Gly, prevents proper strong myosin binding and triggers muscle weakness.Phenotypes of myopathy-related beta-tropomyosin mutants in human and mouse tissue cultures.Disrupted myosin cross-bridge cycling kinetics triggers muscle weakness in nebulin-related myopathy.Congenital myopathy-causing tropomyosin mutations induce thin filament dysfunction via distinct physiological mechanisms.Novel deletion of lysine 7 expands the clinical, histopathological and genetic spectrum of TPM2-related myopathies.First Korean family with a mutation in TPM2 associated with Sheldon-Hall syndrome.Modulating myosin restores muscle function in a mouse model of nemaline myopathy.Sarcomere Dysfunction in Nemaline Myopathy.Distinct underlying mechanisms of limb and respiratory muscle fiber weaknesses in nemaline myopathy.A myopathy-related actin mutation increases contractile function.The fraction of strongly bound cross-bridges is increased in mice that carry the myopathy-linked myosin heavy chain mutation MYH4L342Q.Tropomyosin is a nice marker gene for phylogenetic analysis of molluscs.Skeletal and cardiac α-actin isoforms differently modulate myosin cross-bridge formation and myofibre force production.Myofilament lattice structure in presence of a skeletal myopathy-related tropomyosin mutation.Myosin Head Configurations in Resting and Contracting Murine Skeletal Muscle
P2860
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P2860
A myopathy-linked tropomyosin mutation severely alters thin filament conformational changes during activation.
description
2010 nî lūn-bûn
@nan
2010 թուականի Մայիսին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի մայիսին հրատարակված գիտական հոդված
@hy
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
name
A myopathy-linked tropomyosin ...... nal changes during activation.
@ast
A myopathy-linked tropomyosin ...... nal changes during activation.
@en
A myopathy-linked tropomyosin ...... nal changes during activation.
@nl
type
label
A myopathy-linked tropomyosin ...... nal changes during activation.
@ast
A myopathy-linked tropomyosin ...... nal changes during activation.
@en
A myopathy-linked tropomyosin ...... nal changes during activation.
@nl
prefLabel
A myopathy-linked tropomyosin ...... nal changes during activation.
@ast
A myopathy-linked tropomyosin ...... nal changes during activation.
@en
A myopathy-linked tropomyosin ...... nal changes during activation.
@nl
P2093
P2860
P356
P1476
A myopathy-linked tropomyosin ...... nal changes during activation.
@en
P2093
Hiroyuki Iwamoto
Julien Ochala
Naoto Yagi
P2860
P304
P356
10.1073/PNAS.1001733107
P407
P50
P577
2010-05-10T00:00:00Z