Conserved intramolecular disulfide bond is critical to trafficking and fate of ATP-binding cassette (ABC) transporters ABCB6 and sulfonylurea receptor 1 (SUR1)/ABCC8
about
Where is it and How Does it Get There - Intracellular Localization and Traffic of P-glycoproteinDelineation of the clinical, molecular and cellular aspects of novel JAM3 mutations underlying the autosomal recessive hemorrhagic destruction of the brain, subependymal calcification, and congenital cataractsIdentification of a Disulfide Bridge in Sodium-Coupled Neutral Amino Acid Transporter 2(SNAT2) by Chemical ModificationRole of the N-terminal transmembrane domain in the endo-lysosomal targeting and function of the human ABCB6 protein.Missense mutations in the ABCB6 transporter cause dominant familial pseudohyperkalemia.Shifting the paradigm: the putative mitochondrial protein ABCB6 resides in the lysosomes of cells and in the plasma membrane of erythrocytes.Role of cysteine residues in cell surface expression of the human riboflavin transporter-2 (hRFT2) in intestinal epithelial cells.Mitochondrial localization of ABC transporter ABCG2 and its function in 5-aminolevulinic acid-mediated protoporphyrin IX accumulationIdentification of a disulfide bridge important for transport function of SNAT4 neutral amino acid transporterRole of Derlin-1 protein in proteostasis regulation of ATP-sensitive potassium channels.Cellular and mitochondrial iron homeostasis in vertebratesThe severity of hereditary porphyria is modulated by the porphyrin exporter and Lan antigen ABCB6.Crucial role for phylogenetically conserved cytoplasmic loop 3 in ABCC4 protein expressionEfficient purification and reconstitution of ATP binding cassette transporter B6 (ABCB6) for functional and structural studiesPharmacological rescue of trafficking-impaired ATP-sensitive potassium channels.Cryo-EM structure of the ATP-sensitive potassium channel illuminates mechanisms of assembly and gating.Pharmacological Correction of Trafficking Defects in ATP-sensitive Potassium Channels Caused by Sulfonylurea Receptor 1 Mutations.ABCB6, an ABC Transporter Impacting Drug Response and Disease.
P2860
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P2860
Conserved intramolecular disulfide bond is critical to trafficking and fate of ATP-binding cassette (ABC) transporters ABCB6 and sulfonylurea receptor 1 (SUR1)/ABCC8
description
2011 nî lūn-bûn
@nan
2011 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2011年の論文
@ja
2011年学术文章
@wuu
2011年学术文章
@zh-cn
2011年学术文章
@zh-hans
2011年学术文章
@zh-my
2011年学术文章
@zh-sg
2011年學術文章
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name
Conserved intramolecular disul ...... ylurea receptor 1 (SUR1)/ABCC8
@ast
Conserved intramolecular disul ...... ylurea receptor 1 (SUR1)/ABCC8
@en
Conserved intramolecular disul ...... d fate of ATP-binding cassette
@nl
type
label
Conserved intramolecular disul ...... ylurea receptor 1 (SUR1)/ABCC8
@ast
Conserved intramolecular disul ...... ylurea receptor 1 (SUR1)/ABCC8
@en
Conserved intramolecular disul ...... d fate of ATP-binding cassette
@nl
prefLabel
Conserved intramolecular disul ...... ylurea receptor 1 (SUR1)/ABCC8
@ast
Conserved intramolecular disul ...... ylurea receptor 1 (SUR1)/ABCC8
@en
Conserved intramolecular disul ...... d fate of ATP-binding cassette
@nl
P2093
P2860
P356
P1476
Conserved intramolecular disul ...... ylurea receptor 1 (SUR1)/ABCC8
@en
P2093
Aurelie Dechaume
John D Schuetz
Joseph Bryan
Karobi Moitra
Lydia Aguilar-Bryan
Martine Vaxillaire
P2860
P304
P356
10.1074/JBC.M110.174516
P407
P577
2011-01-03T00:00:00Z