about
Shared and distinct mechanisms of iron acquisition by bacterial and fungal pathogens of humansMicroRNA-210 regulates mitochondrial free radical response to hypoxia and krebs cycle in cancer cells by targeting iron sulfur cluster protein ISCUCharacterization of the human HSC20, an unusual DnaJ type III protein, involved in iron-sulfur cluster biogenesisGlutaredoxin 5 deficiency causes sideroblastic anemia by specifically impairing heme biosynthesis and depleting cytosolic iron in human erythroblastsSDHAF1, encoding a LYR complex-II specific assembly factor, is mutated in SDH-defective infantile leukoencephalopathyMicroRNA-210: a unique and pleiotropic hypoxamirSystematic molecular genetic analysis of congenital sideroblastic anemia: evidence for genetic heterogeneity and identification of novel mutationsHuman iron-sulfur cluster assembly, cellular iron homeostasis, and diseaseMicroRNA-210 controls mitochondrial metabolism during hypoxia by repressing the iron-sulfur cluster assembly proteins ISCU1/2Parkinson's Disease: The Mitochondria-Iron LinkErythroid heme biosynthesis and its disordersMetabolic dysfunction in pulmonary hypertension: the expanding relevance of the Warburg effectIron insufficiency compromises motor neurons and their mitochondrial function in Irp2-null miceEmerging critical roles of Fe-S clusters in DNA replication and repair.Iron traffics in circulation bound to a siderocalin (Ngal)–catechol complexFriedreich’s Ataxia Variants I154F and W155R Diminish Frataxin-Based Activation of the Iron–Sulfur Cluster Assembly ComplexMolecular view of an electron transfer process essential for iron-sulfur protein biogenesisSpecialized function of yeast Isa1 and Isa2 proteins in the maturation of mitochondrial [4Fe-4S] proteins.Tah18 transfers electrons to Dre2 in cytosolic iron-sulfur protein biogenesis.Refractory anemia with ring sideroblasts and RARS with thrombocytosisThe Friedreich's ataxia protein frataxin modulates DNA base excision repair in prokaryotes and mammalsRedox regulation of mitochondrial functionDual localized AtHscB involved in iron sulfur protein biogenesis in ArabidopsisCisd2 deficiency drives premature aging and causes mitochondria-mediated defects in miceFormation, spectroscopic characterization, and solution stability of an [Fe4S4]2+ cluster derived from β-cyclodextrin dithiolate.Cavitating leukoencephalopathy with multiple mitochondrial dysfunction syndrome and NFU1 mutations.Further delineation of a rare recessive encephalomyopathy linked to mutations in GFER thanks to data sharing of whole exome sequencing data.Iron and porphyrin trafficking in heme biogenesis.Mitochondrial ABC Transporter ATM3 Is Essential for Cytosolic Iron-Sulfur Cluster Assembly.Iron redistribution as a therapeutic strategy for treating diseases of localized iron accumulation.Emerging Metabolic Therapies in Pulmonary Arterial Hypertension.Drosophila mitoferrin is essential for male fertility: evidence for a role of mitochondrial iron metabolism during spermatogenesis.Glutaredoxins: roles in iron homeostasisA disruption in iron-sulfur center biogenesis via inhibition of mitochondrial dithiol glutaredoxin 2 may contribute to mitochondrial and cellular iron dysregulation in mammalian glutathione-depleted dopaminergic cells: implications for Parkinson's dThe VHL-dependent regulation of microRNAs in renal cancer.Functional characterization of Friedreich ataxia iPS-derived neuronal progenitors and their integration in the adult brain.Mitochondrial iron trafficking and the integration of iron metabolism between the mitochondrion and cytosol.Biophysical characterization of iron in mitochondria isolated from respiring and fermenting yeast.Humans possess two mitochondrial ferredoxins, Fdx1 and Fdx2, with distinct roles in steroidogenesis, heme, and Fe/S cluster biosynthesis.pH-induced conformational change of IscU at low pH correlates with protonation/deprotonation of two conserved histidine residues.
P2860
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P2860
description
2008 nî lūn-bûn
@nan
2008 թուականի Յուլիսին հրատարակուած գիտական յօդուած
@hyw
2008 թվականի հուլիսին հրատարակված գիտական հոդված
@hy
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
name
Iron-sulfur cluster biogenesis and human disease
@ast
Iron-sulfur cluster biogenesis and human disease
@en
Iron-sulfur cluster biogenesis and human disease
@nl
type
label
Iron-sulfur cluster biogenesis and human disease
@ast
Iron-sulfur cluster biogenesis and human disease
@en
Iron-sulfur cluster biogenesis and human disease
@nl
prefLabel
Iron-sulfur cluster biogenesis and human disease
@ast
Iron-sulfur cluster biogenesis and human disease
@en
Iron-sulfur cluster biogenesis and human disease
@nl
P2860
P1433
P1476
Iron-sulfur cluster biogenesis and human disease
@en
P2093
Tracey A Rouault
Wing Hang Tong
P2860
P304
P356
10.1016/J.TIG.2008.05.008
P577
2008-07-05T00:00:00Z