The Batten disease gene CLN3 is required for the response to oxidative stress.
about
Neuronal ceroid lipofuscinosis protein CLN3 interacts with motor proteins and modifies location of late endosomal compartmentsGlobal profiling of co- and post-translationally N-myristoylated proteomes in human cellsOxidative Stress Related Diseases in NewbornsFruit flies in biomedical research.Oxidative stress in neurodegenerative diseases: mechanisms and therapeutic perspectivesProgress in the Development of Small Molecule Therapeutics for the Treatment of Neuronal Ceroid Lipofuscinoses (NCLs).Neuroinflammatory paradigms in lysosomal storage diseases.Vision loss in juvenile neuronal ceroid lipofuscinosis (CLN3 disease)Mutations in palmitoyl-protein thioesterase 1 alter exocytosis and endocytosis at synapses in Drosophila larvae.Invertebrate models of lysosomal storage disease: what have we learned so far?NCLs and ER: A stressful relationship.A central role for TOR signalling in a yeast model for juvenile CLN3 diseaseProteomic mapping of differentially vulnerable pre-synaptic populations identifies regulators of neuronal stability in vivoin vivo localization of the neuronal ceroid lipofuscinosis proteins, CLN3 and CLN7, at endogenous expression levelsGlial cells are functionally impaired in juvenile neuronal ceroid lipofuscinosis and detrimental to neurons.Microglia in juvenile neuronal ceroid lipofuscinosis are primed toward a pro-inflammatory phenotype.Pharmacological Effects on Ceroid Lipofuscin and Neuronal Structure in Cln3 ∆ex7/8 Mouse Brain Cultures.
P2860
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P2860
The Batten disease gene CLN3 is required for the response to oxidative stress.
description
2011 nî lūn-bûn
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2011 թուականի Մարտին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի մարտին հրատարակված գիտական հոդված
@hy
2011年の論文
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2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
The Batten disease gene CLN3 is required for the response to oxidative stress.
@ast
The Batten disease gene CLN3 is required for the response to oxidative stress.
@en
The Batten disease gene CLN3 is required for the response to oxidative stress.
@nl
type
label
The Batten disease gene CLN3 is required for the response to oxidative stress.
@ast
The Batten disease gene CLN3 is required for the response to oxidative stress.
@en
The Batten disease gene CLN3 is required for the response to oxidative stress.
@nl
prefLabel
The Batten disease gene CLN3 is required for the response to oxidative stress.
@ast
The Batten disease gene CLN3 is required for the response to oxidative stress.
@en
The Batten disease gene CLN3 is required for the response to oxidative stress.
@nl
P2093
P2860
P356
P1476
The Batten disease gene CLN3 is required for the response to oxidative stress
@en
P2093
Haiyang Chen
Nancy Carvajal
Valerie Vivancos
P2860
P304
P356
10.1093/HMG/DDR088
P577
2011-03-03T00:00:00Z