Infectious diseases in patients with IRAK-4, MyD88, NEMO, or IκBα deficiency. - Wikidata - wikimedia - TriplyDB

Infectious diseases in patients with IRAK-4, MyD88, NEMO, or IκBα deficiency.

Infectious diseases in patients with IRAK-4, MyD88, NEMO, or IκBα deficiency.

http://www.wikidata.org/entity/Q35090141

about

Immunodeficiency, autoinflammation and amylopectinosis in humans with inherited HOIL-1 and LUBAC deficiency CCDC22 deficiency in humans blunts activation of proinflammatory NF-κB signaling Primary immunodeficiencies of pattern recognition receptors Mendelian susceptibility to mycobacterial disease: genetic, immunological, and clinical features of inborn errors of IFN-γ immunity Ubiquitin in the immune system Mucocutaneous candidiasis: the IL-17 pathway and implications for targeted immunotherapy The TLR and IL-1 signalling network at a glance Mendelian genetics of human susceptibility to fungal infection Antimicrobial Proteins and Peptides in Early Life: Ontogeny and Translational Opportunities The immunology of influenza virus-associated bacterial pneumonia Neutrophils: Between host defence, immune modulation, and tissue injury MyD88: a central player in innate immune signaling STAT2 deficiency and susceptibility to viral illness in humans Sulphonylurea usage in melioidosis is associated with severe disease and suppressed immune response Dectin-1 Controls TLR9 Trafficking to Phagosomes Containing β-1,3 Glucan TNF and IL-1 exhibit distinct ubiquitin requirements for inducing NEMO-IKK supramolecular structures Structural dynamic analysis of apo and ATP-bound IRAK4 kinase IRAK4 Deficiency in a Patient with Recurrent Pneumococcal Infections: Case Report and Review of the Literature.Comparative genomics RNAi screen identifies Eftud2 as a novel regulator of innate immunity.B cell TLRs and induction of immunoglobulin class-switch DNA recombination.Primary immunodeficiencies underlying fungal infections Invasive pneumococcal disease in children can reveal a primary immunodeficiency.Cytokine production assays reveal discriminatory immune defects in adults with recurrent infections and noninfectious inflammation.TLR-mediated inflammatory responses to Streptococcus pneumoniae are highly dependent on surface expression of bacterial lipoproteins Interaction of Streptococcus agalactiae and Cellular Innate Immunity in Colonization and Disease Innate immunity networks during infection with Borrelia burgdorferi.DNA polymerase-α regulates the activation of type I interferons through cytosolic RNA:DNA synthesis IRAK-4 and MyD88 deficiencies impair IgM responses against T-independent bacterial antigens A narrow repertoire of transcriptional modules responsive to pyogenic bacteria is impaired in patients carrying loss-of-function mutations in MYD88 or IRAK4 Skin fibroblasts from individuals with Chediak-Higashi Syndrome (CHS) exhibit hyposensitive immunogenic response.Defective lymphoid organogenesis underlies the immune deficiency caused by a heterozygous S32I mutation in IκBα.Recurrent invasive pneumococcal disease in children: underlying clinical conditions, and immunological and microbiological characteristics.Rare variants in MYD88, IRAK4 and IKBKG and susceptibility to invasive pneumococcal disease: a population-based case-control study Inherited and acquired immunodeficiencies underlying tuberculosis in childhood.Immunodeficiency among children with recurrent invasive pneumococcal disease.Human HOIP and LUBAC deficiency underlies autoinflammation, immunodeficiency, amylopectinosis, and lymphangiectasia.Interleukin-1 (IL-1) signaling in intestinal stromal cells controls KC/ CXCL1 secretion, which correlates with recruitment of IL-22- secreting neutrophils at early stages of Citrobacter rodentium infection.Sensing of interleukin-1 cytokines during Streptococcus pneumoniae colonization contributes to macrophage recruitment and bacterial clearance.Rapid diagnosis of Propionibacterium acnes infection in patient with hyperpyrexia after hematopoietic stem cell transplantation by next-generation sequencing: a case report.Osteoprotegerin Regulates Pancreatic β-Cell Homeostasis upon Microbial Invasion

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Infectious diseases in patients with IRAK-4, MyD88, NEMO, or IκBα deficiency.

http://www.wikidata.org/entity/Q35090141

description

2011 nî lūn-bûn

@nan

2011 թուականի Յուլիսին հրատարակուած գիտական յօդուած

@hyw

2011 թվականի հուլիսին հրատարակված գիտական հոդված

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2011年の論文

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2011年論文

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2011年論文

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2011年論文

@zh-hk

2011年論文

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2011年論文

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2011年论文

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name

Infectious diseases in patients with IRAK-4, MyD88, NEMO, or IκBα deficiency.

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Infectious diseases in patients with IRAK-4, MyD88, NEMO, or IκBα deficiency.

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Infectious diseases in patients with IRAK-4, MyD88, NEMO, or IκBα deficiency.

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Infectious diseases in patients with IRAK-4, MyD88, NEMO, or IκBα deficiency.

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Infectious diseases in patients with IRAK-4, MyD88, NEMO, or IκBα deficiency.

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Infectious diseases in patients with IRAK-4, MyD88, NEMO, or IκBα deficiency.

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Clinical Microbiology Reviews

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Infectious diseases in patients with IRAK-4, MyD88, NEMO, or IκBα deficiency.

@en

P2860

Human TLR-7-, -8-, and -9-mediated induction of IFN-alpha/beta and -lambda Is IRAK-4 dependent and redundant for protective immunity to viruses

Impaired neutrophil migration and phagocytosis in IRAK-4 deficiency

A novel X-linked disorder of immune deficiency and hypohidrotic ectodermal dysplasia is allelic to incontinentia pigmenti and due to mutations in IKK-gamma (NEMO)

Pyogenic bacterial infections in humans with MyD88 deficiency

Helical assembly in the MyD88–IRAK4–IRAK2 complex in TLR/IL-1R signalling

The role of pattern-recognition receptors in innate immunity: update on Toll-like receptors

Genomic rearrangement in NEMO impairs NF-kappaB activation and is a cause of incontinentia pigmenti. The International Incontinentia Pigmenti (IP) Consortium

Pyogenic bacterial infections in humans with IRAK-4 deficiency

Specific missense mutations in NEMO result in hyper-IgM syndrome with hypohydrotic ectodermal dysplasia

X-linked anhidrotic ectodermal dysplasia with immunodeficiency is caused by impaired NF-kappaB signaling

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490-497

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scholarly article

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10.1128/CMR.00001-11

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3

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24

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Jean-Laurent Casanova

Capucine Picard

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2011-07-01T00:00:00Z

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51472195

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3131061

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