Carnitine transport: pathophysiology and metabolism of known molecular defects.
about
New insights concerning the role of carnitine in the regulation of fuel metabolism in skeletal muscleCarnitine content and expression of mitochondrial beta-oxidation enzymes in placentas of wild-type (OCTN2(+/+)) and OCTN2 Null (OCTN2(-/-)) MiceIncreased maternal consumption of methionine as its hydroxyl analog promoted neonatal intestinal growth without compromising maternal energy homeostasisA moderate excess of dietary lysine lowers plasma and tissue carnitine concentrations in pigs.PPAR alpha mediates transcriptional upregulation of novel organic cation transporters-2 and -3 and enzymes involved in hepatic carnitine synthesis.Dietary oxidised fat up regulates the expression of organic cation transporters in liver and small intestine and alters carnitine concentrations in liver, muscle and plasma of rats.Localization of organic cation/carnitine transporter (OCTN2) in cells forming the blood-brain barrier.Inborn errors of energy metabolism associated with myopathies.Colon OCTN2 gene expression is up-regulated by peroxisome proliferator-activated receptor gamma in humans and mice and contributes to local and systemic carnitine homeostasisExpression of genes involved in hepatic carnitine synthesis and uptake in dairy cows in the transition period and at different stages of lactation.Quantitative structure activity relationship for inhibition of human organic cation/carnitine transporter.A modern approach to the treatment of mitochondrial diseaseIn vivo release of non-neuronal acetylcholine from the human skin as measured by dermal microdialysis: effect of botulinum toxin.Carnitine levels in skeletal muscle, blood, and urine in patients with primary carnitine deficiency during intermission of L-carnitine supplementationEffect of L-carnitine on the hepatic transcript profile in piglets as animal model.Acetyl-L-carnitine increases mitochondrial protein acetylation in the aged rat heart.Hyperammonemic encephalopathy caused by carnitine deficiency.Functional genetic variation in the basal promoter of the organic cation/carnitine transporters OCTN1 (SLC22A4) and OCTN2 (SLC22A5).Increased insulin sensitivity in mice lacking collectrin, a downstream target of HNF-1alpha.Carnitine insufficiency caused by aging and overnutrition compromises mitochondrial performance and metabolic controlInfluence of l-carnitine on metabolism and performance of sows.Obesity and lipid stress inhibit carnitine acetyltransferase activityGenetics and metabolic cardiomyopathies.Pathophysiology of fatty acid oxidation disorders and resultant phenotypic variability.Renal transport of organic anions and cations.Regulation of Genes Involved in Carnitine Homeostasis by PPARα across Different Species (Rat, Mouse, Pig, Cattle, Chicken, and Human)Plasma carnitine ester profile in homozygous and heterozygous OCTN2 deficiency.Primary Carnitine deficiency in the Faroe Islands: health and cardiac status in 76 adult patients diagnosed by screening.OCTN3: A Na+-independent L-carnitine transporter in enterocytes basolateral membrane.Supplementation of L-carnitine in pigs: absorption of carnitine and effect on plasma and tissue carnitine concentrations.Serum and muscle carnitine levels in epileptic children receiving sodium valproate.Primary Carnitine Deficiency: Is Foetal Development Affected and Can Newborn Screening Be Improved?The adverse effects of long-term l-carnitine supplementation on liver and kidney function in rats.Primary carnitine deficiency and pivalic acid exposure causing encephalopathy and fatal cardiac events.L-carnitine-L-tartrate promotes human hair growth in vitro.A novel mouse model of X-linked cardiac hypertrophy.Studies on the chemopreventive effect of carnitine on tumorigenesis in vivo, using two experimental murine models of colon cancer.Effects of fish oil and conjugated linoleic acids on carnitine homeostasis in laying hens.Omics-based responses induced by bosentan in human hepatoma HepaRG cell culturesDietary L-carnitine alters gene expression in skeletal muscle of piglets
P2860
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P2860
Carnitine transport: pathophysiology and metabolism of known molecular defects.
description
2003 nî lūn-bûn
@nan
2003 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2003 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2003年の論文
@ja
2003年論文
@yue
2003年論文
@zh-hant
2003年論文
@zh-hk
2003年論文
@zh-mo
2003年論文
@zh-tw
2003年论文
@wuu
name
Carnitine transport: pathophysiology and metabolism of known molecular defects.
@ast
Carnitine transport: pathophysiology and metabolism of known molecular defects.
@en
type
label
Carnitine transport: pathophysiology and metabolism of known molecular defects.
@ast
Carnitine transport: pathophysiology and metabolism of known molecular defects.
@en
prefLabel
Carnitine transport: pathophysiology and metabolism of known molecular defects.
@ast
Carnitine transport: pathophysiology and metabolism of known molecular defects.
@en
P356
P1476
Carnitine transport: pathophysiology and metabolism of known molecular defects.
@en
P2093
P2888
P304
P356
10.1023/A:1024481016187
P577
2003-01-01T00:00:00Z
P6179
1042633968