L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia.
about
Proposed guidelines for the diagnosis and management of methylmalonic and propionic acidemiaIdentification of 3-methylglutarylcarnitine. A new diagnostic metabolite of 3-hydroxy-3-methylglutaryl-coenzyme A lyase deficiencyL-carnitine therapy in isovaleric acidemiaTranslating the basic knowledge of mitochondrial functions to metabolic therapy: role of L-carnitineAcute management of propionic acidemia.Plasma and muscle free carnitine deficiency due to renal Fanconi syndrome.Adeno-associated virus serotype 8 gene transfer rescues a neonatal lethal murine model of propionic acidemia.On the protective effect of omega-3 against propionic acid-induced neurotoxicity in rat pups.Short-chain fatty acid fermentation products of the gut microbiome: implications in autism spectrum disorders.Impaired Exercise Performance and Skeletal Muscle Mitochondrial Function in Rats with Secondary Carnitine Deficiency.Organic acidurias: a review. Part 2.Plasma carnitine in fasting neonatal and adult northern elephant seals.Equine atypical myopathy in the UK: Epidemiological characteristics of cases reported from 2011 to 2015 and factors associated with survival.Methylmalonic and propionic acidemias: clinical management update.Short-term rescue of neonatal lethality in a mouse model of propionic acidemia by gene therapy.Effects of propionate and carnitine on the hepatic oxidation of short- and medium-chain-length fatty acidsInhibition of oxidative metabolism by propionic acid and its reversal by carnitine in isolated rat hepatocytes.Contractile function and energy metabolism of skeletal muscle in rats with secondary carnitine deficiency.Propionyl-CoA carboxylase - A review.L-Carnitine and Acetyl-L-carnitine Roles and Neuroprotection in Developing Brain.Development of a newborn screening follow-up algorithm for the diagnosis of isobutyryl-CoA dehydrogenase deficiency.Disorders of branched chain amino acid metabolism.The Impact of Carnitine on Dietary Fiber and Gut Bacteria Metabolism and Their Mutual Interaction in Monogastrics.
P2860
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P2860
L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia.
description
1984 nî lūn-bûn
@nan
1984 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
1984 թվականի հունիսին հրատարակված գիտական հոդված
@hy
1984年の論文
@ja
1984年論文
@yue
1984年論文
@zh-hant
1984年論文
@zh-hk
1984年論文
@zh-mo
1984年論文
@zh-tw
1984年论文
@wuu
name
L-carnitine enhances excretion ...... rnitine in propionic acidemia.
@ast
L-carnitine enhances excretion ...... rnitine in propionic acidemia.
@en
type
label
L-carnitine enhances excretion ...... rnitine in propionic acidemia.
@ast
L-carnitine enhances excretion ...... rnitine in propionic acidemia.
@en
prefLabel
L-carnitine enhances excretion ...... rnitine in propionic acidemia.
@ast
L-carnitine enhances excretion ...... rnitine in propionic acidemia.
@en
P2093
P2860
P356
P1476
L-carnitine enhances excretion ...... rnitine in propionic acidemia.
@en
P2093
C L Hoppel
D A Maltby
D S Millington
P2860
P304
P356
10.1172/JCI111387
P407
P577
1984-06-01T00:00:00Z