Novel oxysterols observed in tissues and fluids of AY9944-treated rats: a model for Smith-Lemli-Opitz syndrome.
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Lipid biomarkers of oxidative stress in a genetic mouse model of Smith-Lemli-Opitz syndrome7-Dehydrocholesterol-derived oxysterols and retinal degeneration in a rat model of Smith-Lemli-Opitz syndromeSterols and oxysterols in plasma from Smith-Lemli-Opitz syndrome patientsThe Effect of Small Molecules on Sterol Homeostasis: Measuring 7-Dehydrocholesterol in Dhcr7-Deficient Neuro2a Cells and Human FibroblastsIon-current-based proteomic profiling of the retina in a rat model of Smith-Lemli-Opitz syndrome.Cholesterol in the retina: the best is yet to come.Antioxidant supplementation ameliorates molecular deficits in Smith-Lemli-Opitz syndromeElevated Autophagy and Mitochondrial Dysfunction in the Smith-Lemli-Opitz Syndrome.Probing lipid-protein adduction with alkynyl surrogates: application to Smith-Lemli-Opitz syndrome.Free radical oxidation of cholesterol and its precursors: Implications in cholesterol biosynthesis disorders.Inhibitors of 7-Dehydrocholesterol Reductase: Screening of a Collection of Pharmacologically Active Compounds in Neuro2a Cells.Oxidation of 7-dehydrocholesterol and desmosterol by human cytochrome P450 46A1.Assays of plasma dehydrocholesteryl esters and oxysterols from Smith-Lemli-Opitz syndrome patientsMetabolism of oxysterols derived from nonenzymatic oxidation of 7-dehydrocholesterol in cells.Identification of Environmental Quaternary Ammonium Compounds as Direct Inhibitors of Cholesterol Biosynthesis.Endogenous B-ring oxysterols inhibit the Hedgehog component Smoothened in a manner distinct from cyclopamine or side-chain oxysterols.A highly sensitive method for analysis of 7-dehydrocholesterol for the study of Smith-Lemli-Opitz syndromeDifferential cytotoxic effects of 7-dehydrocholesterol-derived oxysterols on cultured retina-derived cells: Dependence on sterol structure, cell type, and density.Antioxidants: The Missing Key to Improved Therapeutic Intervention in Smith-Lemli-Opitz Syndrome?Effect of psychotropic drug treatment on sterol metabolism.Prevention of Retinal Degeneration in a Rat Model of Smith-Lemli-Opitz Syndrome.Liver transplantation in defects of cholesterol biosynthesis: the case of lathosterolosis.7DHC-induced changes of Kv1.3 operation contributes to modified T cell function in Smith-Lemli-Opitz syndrome.Assessment of altered lipid homeostasis by HILIC-ion mobility-mass spectrometry-based lipidomics.Oxysterols and Retinal Degeneration in a Rat Model of Smith-Lemli-Opitz Syndrome: Implications for an Improved Therapeutic Intervention
P2860
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P2860
Novel oxysterols observed in tissues and fluids of AY9944-treated rats: a model for Smith-Lemli-Opitz syndrome.
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2011 nî lūn-bûn
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2011 թուականի Օգոստոսին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի օգոստոսին հրատարակված գիտական հոդված
@hy
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
Novel oxysterols observed in t ...... or Smith-Lemli-Opitz syndrome.
@ast
Novel oxysterols observed in t ...... or Smith-Lemli-Opitz syndrome.
@en
type
label
Novel oxysterols observed in t ...... or Smith-Lemli-Opitz syndrome.
@ast
Novel oxysterols observed in t ...... or Smith-Lemli-Opitz syndrome.
@en
prefLabel
Novel oxysterols observed in t ...... or Smith-Lemli-Opitz syndrome.
@ast
Novel oxysterols observed in t ...... or Smith-Lemli-Opitz syndrome.
@en
P2093
P2860
P356
P1476
Novel oxysterols observed in t ...... or Smith-Lemli-Opitz syndrome.
@en
P2093
Lowell G Sheflin
Ned A Porter
Steven J Fliesler
P2860
P304
P356
10.1194/JLR.M018366
P577
2011-08-04T00:00:00Z