The galactocerebrosidase enzyme contributes to the maintenance of a functional hematopoietic stem cell niche.
about
Structural snapshots illustrate the catalytic cycle of β-galactocerebrosidase, the defective enzyme in Krabbe disease.Combined gene/cell therapies provide long-term and pervasive rescue of multiple pathological symptoms in a murine model of globoid cell leukodystrophy.Gene therapy for lysosomal storage disorders: a good start.Many mechanisms mediating mobilization: an alliterative review.Azasugar inhibitors as pharmacological chaperones for Krabbe diseaseDesign of a regulated lentiviral vector for hematopoietic stem cell gene therapy of globoid cell leukodystrophyMissense mutation in mouse GALC mimics human gene defect and offers new insights into Krabbe diseaseInhibition of angiogenesis by β-galactosylceramidase deficiency in globoid cell leukodystrophy.Hematopoietic Stem cell transplantation and lentiviral vector-based gene therapy for Krabbe's disease: Present convictions and future prospects.MicroRNAs and Molecular Mechanisms of Neurodegeneration.Endothelial cell dysfunction in globoid cell leukodystrophy.Krabbe's leukodystrophy: Approaches and models in vitro.Biochemical, cell biological, pathological, and therapeutic aspects of Krabbe's disease.Perspective on innovative therapies for globoid cell leukodystrophy.Gene therapy for lysosomal storage disorders: recent advances for metachromatic leukodystrophy and mucopolysaccaridosis I.Genomewide association study identifies GALC as susceptibility gene for mucous membrane pemphigoid.Long-Term Improvement of Neurological Signs and Metabolic Dysfunction in a Mouse Model of Krabbe's Disease after Global Gene Therapy.Nanocomposites Based on Biodegradable Polymers.
P2860
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P2860
The galactocerebrosidase enzyme contributes to the maintenance of a functional hematopoietic stem cell niche.
description
2010 nî lūn-bûn
@nan
2010 թուականի Մայիսին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի մայիսին հրատարակված գիտական հոդված
@hy
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
name
The galactocerebrosidase enzym ...... hematopoietic stem cell niche.
@ast
The galactocerebrosidase enzym ...... hematopoietic stem cell niche.
@en
type
label
The galactocerebrosidase enzym ...... hematopoietic stem cell niche.
@ast
The galactocerebrosidase enzym ...... hematopoietic stem cell niche.
@en
prefLabel
The galactocerebrosidase enzym ...... hematopoietic stem cell niche.
@ast
The galactocerebrosidase enzym ...... hematopoietic stem cell niche.
@en
P2093
P2860
P1433
P1476
The galactocerebrosidase enzym ...... hematopoietic stem cell niche.
@en
P2093
Aldo Orlacchio
Alessandra Biffi
Bernhard Gentner
Hyejung Park
Ilaria Visigalli
Lucia Sergi Sergi
Martina Cesani
Sabata Martino
Silvia Ungari
P2860
P304
P356
10.1182/BLOOD-2009-12-256461
P407
P577
2010-05-28T00:00:00Z