Myocyte-mediated arginase expression controls hyperargininemia but not hyperammonemia in arginase-deficient mice.
about
Strategies to rescue the consequences of inducible arginase-1 deficiency in miceFunctional Human and Murine Tissue-Engineered Liver Is Generated from Adult Stem/Progenitor Cells.Proof-of-Concept Gene Editing for the Murine Model of Inducible Arginase-1 DeficiencyProgress and prospects of gene therapy clinical trials for the muscular dystrophies.Minimal ureagenesis is necessary for survival in the murine model of hyperargininemia treated by AAV-based gene therapy.Augmentation of transgene-encoded protein after neonatal injection of adeno-associated virus improves hepatic copy number without immune responses.Rescue of the Functional Alterations of Motor Cortical Circuits in Arginase Deficiency by Neonatal Gene Therapy.Human recombinant arginase enzyme reduces plasma arginine in mouse models of arginase deficiency.Liver-specific knockout of arginase-1 leads to a profound phenotype similar to inducible whole body arginase-1 deficiency.Restoring Ureagenesis in Hepatocytes by CRISPR/Cas9-mediated Genomic Addition to Arginase-deficient Induced Pluripotent Stem Cells.Muscle-specific CRISPR/Cas9 dystrophin gene editing ameliorates pathophysiology in a mouse model for Duchenne muscular dystrophy.
P2860
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P2860
Myocyte-mediated arginase expression controls hyperargininemia but not hyperammonemia in arginase-deficient mice.
description
2014 nî lūn-bûn
@nan
2014年の論文
@ja
2014年論文
@yue
2014年論文
@zh-hant
2014年論文
@zh-hk
2014年論文
@zh-mo
2014年論文
@zh-tw
2014年论文
@wuu
2014年论文
@zh
2014年论文
@zh-cn
name
Myocyte-mediated arginase expr ...... ia in arginase-deficient mice.
@ast
Myocyte-mediated arginase expr ...... ia in arginase-deficient mice.
@en
type
label
Myocyte-mediated arginase expr ...... ia in arginase-deficient mice.
@ast
Myocyte-mediated arginase expr ...... ia in arginase-deficient mice.
@en
prefLabel
Myocyte-mediated arginase expr ...... ia in arginase-deficient mice.
@ast
Myocyte-mediated arginase expr ...... ia in arginase-deficient mice.
@en
P2093
P2860
P356
P1433
P1476
Myocyte-mediated arginase expr ...... ia in arginase-deficient mice.
@en
P2093
Chuhong Hu
Denise S Tai
Gerald S Lipshutz
Jennifer Kasten
Quynh G Nguyen
Ragini Bhargava
Stephen D Cederbaum
Stephen D Hauschka
Wayne W Grody
P2860
P304
P356
10.1038/MT.2014.99
P577
2014-06-03T00:00:00Z