about
Cytosolic signaling protein Ecsit also localizes to mitochondria where it interacts with chaperone NDUFAF1 and functions in complex I assemblyIdentification of mitochondrial complex I assembly intermediates by tracing tagged NDUFS3 demonstrates the entry point of mitochondrial subunitsAnalysis of the assembly profiles for mitochondrial- and nuclear-DNA-encoded subunits into complex IS-nitrosation of mitochondrial complex I depends on its structural conformation.Crystallization of the NADH-oxidizing domain of the Na+-translocating NADH:ubiquinone oxidoreductase from Vibrio cholerae.Mutations in Complex I Assembly Factor TMEM126B Result in Muscle Weakness and Isolated Complex I DeficiencyAIF deficiency compromises oxidative phosphorylation.Mouse models for nuclear DNA-encoded mitochondrial complex I deficiency.Nuclear suppression of mitochondrial defects in cells without the ND6 subunit.Targeting the NAD7 subunit to mitochondria restores a functional complex I and a wild type phenotype in the Nicotiana sylvestris CMS II mutant lacking nad7.Restoration of mitochondrial function in cells with complex I deficiency.Mitochondrial network complexity and pathological decrease in complex I activity are tightly correlated in isolated human complex I deficiency.
P2860
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P2860
description
2004 nî lūn-bûn
@nan
2004年の論文
@ja
2004年論文
@yue
2004年論文
@zh-hant
2004年論文
@zh-hk
2004年論文
@zh-mo
2004年論文
@zh-tw
2004年论文
@wuu
2004年论文
@zh
2004年论文
@zh-cn
name
Complex I assembly: a puzzling problem.
@ast
Complex I assembly: a puzzling problem.
@en
type
label
Complex I assembly: a puzzling problem.
@ast
Complex I assembly: a puzzling problem.
@en
prefLabel
Complex I assembly: a puzzling problem.
@ast
Complex I assembly: a puzzling problem.
@en
P2093
P1476
Complex I assembly: a puzzling problem
@en
P2093
Jan Smeitink
Leo Nijtmans
Rutger Vogel
P304
P356
10.1097/00019052-200404000-00016
P577
2004-04-01T00:00:00Z