The pathology of the feline model of mucopolysaccharidosis I
about
Decreased performance in IDUA knockout mouse mimic limitations of joint function and locomotion in patients with Hurler syndromeComparison of Endovascular and Intraventricular Gene Therapy With Adeno-Associated Virus-α-L-Iduronidase for Hurler DiseaseLiver-directed gene therapy corrects cardiovascular lesions in feline mucopolysaccharidosis type ILong-term effects of bone marrow transplantation in dogs with mucopolysaccharidosis I.Characterization of an immunodeficient mouse model of mucopolysaccharidosis type I suitable for preclinical testing of human stem cell and gene therapy.Biodistribution and pharmacodynamics of recombinant human alpha-L-iduronidase (rhIDU) in mucopolysaccharidosis type I-affected cats following multiple intrathecal administrationsMucopolysaccharidosis type I subtypes. Presence of immunologically cross-reactive material and in vitro enhancement of the residual alpha-L-iduronidase activities.Morphologic and biochemical studies of canine mucopolysaccharidosis I.Gene therapy for lysosomal storage diseases (LSDs) in large animal models.Animal models for mucopolysaccharidosis disorders and their clinical relevance.Clinical characterization of cardiovascular abnormalities associated with feline mucopolysaccharidosis I and VIBone marrow transplantation for feline mucopolysaccharidosis I.Glycosaminoglycan-mediated loss of cathepsin K collagenolytic activity in MPS I contributes to osteoclast and growth plate abnormalities.Renal failure associated with mucopolysaccharidosis type I in a cat from a MPS I research colony.Pathogenesis and treatment of spine disease in the mucopolysaccharidoses.Neonatal tolerance induction enables accurate evaluation of gene therapy for MPS I in a canine model.
P2860
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P2860
The pathology of the feline model of mucopolysaccharidosis I
description
1983 nî lūn-bûn
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1983年の論文
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1983年学术文章
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1983年学术文章
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1983年学术文章
@zh-cn
1983年学术文章
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1983年学术文章
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1983年学术文章
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1983年學術文章
@yue
1983年學術文章
@zh-hant
name
The pathology of the feline model of mucopolysaccharidosis I
@ast
The pathology of the feline model of mucopolysaccharidosis I
@en
type
label
The pathology of the feline model of mucopolysaccharidosis I
@ast
The pathology of the feline model of mucopolysaccharidosis I
@en
prefLabel
The pathology of the feline model of mucopolysaccharidosis I
@ast
The pathology of the feline model of mucopolysaccharidosis I
@en
P2093
P2860
P1476
The pathology of the feline model of mucopolysaccharidosis I
@en
P2093
D F Patterson
G D Aguirre
M E Haskins
R J Desnick
P2860
P407
P577
1983-07-01T00:00:00Z