Peroxisome biogenesis disorders: the role of peroxisomes and metabolic dysfunction in developing brain.
about
Peroxisomes in brain development and functionPeroxisomes and sexual development in fungiIdentification of novel mutations and sequence variation in the Zellweger syndrome spectrum of peroxisome biogenesis disordersThe peroxisome: still a mysterious organelleIdentification of a novel risk locus for multiple sclerosis at 13q31.3 by a pooled genome-wide scan of 500,000 single nucleotide polymorphismsPEX13 deficiency in mouse brain as a model of Zellweger syndrome: abnormal cerebellum formation, reactive gliosis and oxidative stress.Deletion of a single allele of the Pex11β gene is sufficient to cause oxidative stress, delayed differentiation and neuronal death in mouse brainBile acids: the role of peroxisomes.MoPex19, which is essential for maintenance of peroxisomal structure and woronin bodies, is required for metabolism and development in the rice blast fungus.Tauroursodeoxycholic bile acid arrests axonal degeneration by inhibiting the unfolded protein response in X-linked adrenoleukodystrophy.PPARα activation induces N(ε)-Lys-acetylation of rat liver peroxisomal multifunctional enzyme type 1.Epilepsy in children--when should we think neurometabolic disease?Peroxisomes and disease - an overview.Peroxisomal Disorders: A Review on Cerebellar Pathologies.Probing peroxisome dynamics and biogenesis by fluorescence imaging.Pex14/17, a filamentous fungus-specific peroxin, is required for the import of peroxisomal matrix proteins and full virulence of Magnaporthe oryzae.Spectrum of PEX1 and PEX6 variants in Heimler syndrome.Oral Cholic Acid Is Efficacious and Well Tolerated in Patients With Bile Acid Synthesis and Zellweger Spectrum DisordersThe importomer peroxins are differentially required for peroxisome assembly and meiotic development in Podospora anserina: insights into a new peroxisome import pathway.Long-Term Cholic Acid Therapy in Zellweger Spectrum Disorders
P2860
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P2860
Peroxisome biogenesis disorders: the role of peroxisomes and metabolic dysfunction in developing brain.
description
2005 nî lūn-bûn
@nan
2005年の論文
@ja
2005年論文
@yue
2005年論文
@zh-hant
2005年論文
@zh-hk
2005年論文
@zh-mo
2005年論文
@zh-tw
2005年论文
@wuu
2005年论文
@zh
2005年论文
@zh-cn
name
Peroxisome biogenesis disorder ...... sfunction in developing brain.
@ast
Peroxisome biogenesis disorder ...... sfunction in developing brain.
@en
type
label
Peroxisome biogenesis disorder ...... sfunction in developing brain.
@ast
Peroxisome biogenesis disorder ...... sfunction in developing brain.
@en
prefLabel
Peroxisome biogenesis disorder ...... sfunction in developing brain.
@ast
Peroxisome biogenesis disorder ...... sfunction in developing brain.
@en
P2093
P1476
Peroxisome biogenesis disorder ...... sfunction in developing brain.
@en
P2093
P2888
P304
P356
10.1007/S10545-005-7059-Y
P577
2005-01-01T00:00:00Z