Adaptation and increased susceptibility to infection associated with constitutive expression of misfolded SP-C.
about
ERdj4 and ERdj5 are required for endoplasmic reticulum-associated protein degradation of misfolded surfactant protein CMeckel-Gruber syndrome protein MKS3 is required for endoplasmic reticulum-associated degradation of surfactant protein CMolecular biomarkers in idiopathic pulmonary fibrosisFrom HLA-B27 to spondyloarthritis: a journey through the ER.Genetic disorders of surfactant dysfunctionThe Brichos domain-containing C-terminal part of pro-surfactant protein C binds to an unfolded poly-val transmembrane segmentAlveolar surfactant homeostasis and the pathogenesis of pulmonary diseaseNeonatal oxygen increases sensitivity to influenza A virus infection in adult mice by suppressing epithelial expression of Ear1C-terminal, endoplasmic reticulum-lumenal domain of prosurfactant protein C - structural features and membrane interactions.Epithelial endoplasmic reticulum stress and apoptosis in sporadic idiopathic pulmonary fibrosis.Image-based screening for the identification of novel proteasome inhibitors.Critical structural and functional roles for the N-terminal insertion sequence in surfactant protein B analogs.Nedd4-2-mediated ubiquitination facilitates processing of surfactant protein-CA non-BRICHOS surfactant protein c mutation disrupts epithelial cell function and intercellular signalingAAV exploits subcellular stress associated with inflammation, endoplasmic reticulum expansion, and misfolded proteins in models of cystic fibrosis.The molecular era of surfactant biology.Pathogenesis of idiopathic pulmonary fibrosisSurfactant protein A2 mutations associated with pulmonary fibrosis lead to protein instability and endoplasmic reticulum stress.Interstitial lung diseases in children.Transmembrane BAX inhibitor motif containing (TMBIM) family proteins perturbs a trans-Golgi network enzyme, Gb3 synthase, and reduces Gb3 biosynthesisDiseases of pulmonary surfactant homeostasis.Heterozygosity for ABCA3 mutations modifies the severity of lung disease associated with a surfactant protein C gene (SFTPC) mutation.A non-BRICHOS SFTPC mutant (SP-CI73T) linked to interstitial lung disease promotes a late block in macroautophagy disrupting cellular proteostasis and mitophagyA nonaggregating surfactant protein C mutant is misdirected to early endosomes and disrupts phospholipid recycling.Surfactant dysfunction.Genetic Basis of Children's Interstitial Lung Disease.Lost after translation: insights from pulmonary surfactant for understanding the role of alveolar epithelial dysfunction and cellular quality control in fibrotic lung disease.Synthetic lung surfactant reduces alveolar-capillary protein leakage in surfactant-deficient rabbits.4-Phenylbutyric acid treatment rescues trafficking and processing of a mutant surfactant protein-C.Genetic studies provide clues on the pathogenesis of idiopathic pulmonary fibrosis.The alveolar epithelium determines susceptibility to lung fibrosis in Hermansky-Pudlak syndrome.Surfactant Protein C-associated interstitial lung disease; three different phenotypes of the same SFTPC mutation.Genetic replacement of surfactant protein-C reduces respiratory syncytial virus induced lung injuryEndoplasmic reticulum stress induces PRNP prion protein gene expression in breast cancer.HLA-B27 misfolding and spondyloarthropathies.Lung fibrosis-associated surfactant protein A1 and C variants induce latent transforming growth factor β1 secretion in lung epithelial cells.Surfactant protein C-deficient mice are susceptible to respiratory syncytial virus infectionPLAGL2 expression-induced lung epithelium damages at bronchiolar alveolar duct junction in emphysema: bNip3- and SP-C-associated cell death/injury activity.Hyperoxia augments ER-stress-induced cell death independent of BiP loss.ER stress and the unfolded protein response in intestinal inflammation.
P2860
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P2860
Adaptation and increased susceptibility to infection associated with constitutive expression of misfolded SP-C.
description
2006 nî lūn-bûn
@nan
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
2006年论文
@zh
2006年论文
@zh-cn
name
Adaptation and increased susce ...... expression of misfolded SP-C.
@ast
Adaptation and increased susce ...... expression of misfolded SP-C.
@en
type
label
Adaptation and increased susce ...... expression of misfolded SP-C.
@ast
Adaptation and increased susce ...... expression of misfolded SP-C.
@en
prefLabel
Adaptation and increased susce ...... expression of misfolded SP-C.
@ast
Adaptation and increased susce ...... expression of misfolded SP-C.
@en
P2093
P2860
P356
P1476
Adaptation and increased susce ...... expression of misfolded SP-C.
@en
P2093
Cheng-Lun Na
Hector R Wong
James P Bridges
Timothy E Weaver
P2860
P304
P356
10.1083/JCB.200508016
P407
P577
2006-01-01T00:00:00Z