Critical evaluation of the use of cell cultures for inclusion in clinical trials of patients affected by collagen VI myopathies
about
Monoamine oxidase inhibition prevents mitochondrial dysfunction and apoptosis in myoblasts from patients with collagen VI myopathies.Sarcopenia and sarcopenic obesity in patients with muscular dystrophy.Mitochondrial dysfunction and defective autophagy in the pathogenesis of collagen VI muscular dystrophies.Melanocytes from Patients Affected by Ullrich Congenital Muscular Dystrophy and Bethlem Myopathy have Dysfunctional Mitochondria That Can be Rescued with Cyclophilin Inhibitors.Defects in calcium homeostasis and mitochondria can be reversed in Pompe disease.Autophagy activation in COL6 myopathic patients by a low-protein-diet pilot trial.Ultrastructural changes in muscle cells of patients with collagen VI-related myopathies.NIM811, a cyclophilin inhibitor without immunosuppressive activity, is beneficial in collagen VI congenital muscular dystrophy models.Body composition, muscle strength, and physical function of patients with Bethlem myopathy and Ullrich congenital muscular dystrophy.Extracellular Collagen VI Has Prosurvival and Autophagy Instructive Properties in Mouse Fibroblasts
P2860
Q34266732-8E03B680-9446-48C0-BFD3-D16D361A9085Q34299706-0C9AAAA4-D725-4E1D-A391-D90A94B2F87FQ34338854-BF99F33A-0ED5-4DFD-A5B0-B4A2DB2EAFD1Q34547398-8DEFD1F8-2E5B-42D2-83A2-A4D08A014FA2Q35853122-1BE82BC6-3BE2-48B2-93A3-83D73297E6EEQ37520725-EBB8BD6E-AA6C-4F15-B666-A45E4917AEDCQ37613885-47121CEA-22B1-448F-8B2C-9FFC6A1BD5CDQ47073612-6B30F31D-B543-4B78-8792-F5B2B26EED05Q54690359-95F67E25-87D8-4D7D-A47F-83DC08DFCB38Q58769569-C294314F-1192-4CFD-A47D-073D441399BC
P2860
Critical evaluation of the use of cell cultures for inclusion in clinical trials of patients affected by collagen VI myopathies
description
2012 nî lūn-bûn
@nan
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
2012年论文
@zh
2012年论文
@zh-cn
name
Critical evaluation of the use ...... cted by collagen VI myopathies
@ast
Critical evaluation of the use ...... cted by collagen VI myopathies
@en
type
label
Critical evaluation of the use ...... cted by collagen VI myopathies
@ast
Critical evaluation of the use ...... cted by collagen VI myopathies
@en
prefLabel
Critical evaluation of the use ...... cted by collagen VI myopathies
@ast
Critical evaluation of the use ...... cted by collagen VI myopathies
@en
P2093
P2860
P50
P356
P1476
Critical evaluation of the use ...... cted by collagen VI myopathies
@en
P2093
A Urciuolo
F Gualandi
N M Maraldi
P Sabatelli
P2860
P304
P356
10.1002/JCP.23039
P577
2012-07-01T00:00:00Z