Pharmacological chaperones facilitate the post-ER transport of recombinant N370S mutant β-glucocerebrosidase in plant cells: evidence that N370S is a folding mutant.

Pharmacological chaperones facilitate the post-ER transport of recombinant N370S mutant β-glucocerebrosidase in plant cells: evidence that N370S is a folding mutant.

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http://www.wikidata.org/entity/Q36182964
Insights into mucopolysaccharidosis I from the structure and action of α-L-iduronidaseGlucocerebrosidase is shaking up the synucleinopathiesAlteration of the proteostasis network of plant cells promotes the post-endoplasmic reticulum trafficking of recombinant mutant (L444P) human β-glucocerebrosidase.Gaucher iPSC-derived macrophages produce elevated levels of inflammatory mediators and serve as a new platform for therapeutic development.Mutant glucocerebrosidase in Gaucher disease recruits Hsp27 to the Hsp90 chaperone complex for proteasomal degradation[More than expectorant: new scientific data on ambroxol in the context of the treatment of bronchopulmonary diseases].Progress and potential of non-inhibitory small molecule chaperones for the treatment of Gaucher disease and its implications for Parkinson disease.Glucosylsphingosine promotes α-synuclein pathology in mutant GBA-associated Parkinson's disease.Production and Purification of Recombinant Glucocerebrosidase in Transgenic Rice Cell Suspension Cultures.New Directions in Gaucher Disease.Gaucher disease: Progress and ongoing challenges.Bicyclic derivatives of L-idonojirimycin as pharmacological chaperones for neuronopathic forms of Gaucher disease.Stabilization of Glucocerebrosidase by Active Site Occupancy.Ambroxol as a pharmacological chaperone for mutant glucocerebrosidase.A systematic investigation of iminosugar click clusters as pharmacological chaperones for the treatment of Gaucher disease.The contribution of mutant GBA to the development of Parkinson disease in Drosophila.Pharmacotherapy of Gaucher Disease: Current and Future Options.
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Pharmacological chaperones facilitate the post-ER transport of recombinant N370S mutant β-glucocerebrosidase in plant cells: evidence that N370S is a folding mutant.

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http://www.wikidata.org/entity/Q36182964
description
2012 nî lūn-bûn
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2012年の論文
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2012年論文
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2012年論文
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2012年論文
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2012年論文
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2012年論文
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2012年论文
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2012年论文
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2012年论文
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name
Pharmacological chaperones fac ...... hat N370S is a folding mutant.
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Pharmacological chaperones fac ...... hat N370S is a folding mutant.
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type
label
Pharmacological chaperones fac ...... hat N370S is a folding mutant.
@ast
Pharmacological chaperones fac ...... hat N370S is a folding mutant.
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prefLabel
Pharmacological chaperones fac ...... hat N370S is a folding mutant.
@ast
Pharmacological chaperones fac ...... hat N370S is a folding mutant.
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Pharmacological chaperones fac ...... hat N370S is a folding mutant.
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P31
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10.1016/J.YMGME.2012.04.018
P433
P478
P577
P5875
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P921
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