Nebulin regulates the assembly and lengths of the thin filaments in striated muscle
about
Nebulin regulates thin filament length, contractility, and Z-disk structure in vivo.Nebulin-deficient mice exhibit shorter thin filament lengths and reduced contractile function in skeletal muscleIdentification of Xin-repeat proteins as novel ligands of the SH3 domains of nebulin and nebulette and analysis of their interaction during myofibril formation and remodelingThe Nebulin family: an actin support groupComprehensive Transcriptome Analysis of Sex-Biased Expressed Genes Reveals Discrete Biological and Physiological Features of Male and Female Schistosoma japonicumTropomodulin isoforms regulate thin filament pointed-end capping and skeletal muscle physiologyMammalian formin Fhod3 plays an essential role in cardiogenesis by organizing myofibrillogenesis.Bin1 SRC homology 3 domain acts as a scaffold for myofiber sarcomere assemblyNeb: a zebrafish model of nemaline myopathy due to nebulin mutation.Aberrant developmental titin splicing and dysregulated sarcomere length in Thymosin β4 knockout mice.Visualization of cardiac muscle thin filaments and measurement of their lengths by electron tomographyNebulin regulates actin filament lengths by a stabilization mechanism.New insights into the structural roles of nebulin in skeletal muscle.Dynamic regulation of sarcomeric actin filaments in striated muscleCofilin-2 controls actin filament length in muscle sarcomeres.Nebulin, a major player in muscle health and diseaseMuscle giants: molecular scaffolds in sarcomerogenesis.The desmin coil 1B mutation K190A impairs nebulin Z-disc assembly and destabilizes actin thin filaments.Investigation of Pathogenic Genes in Chinese sporadic Hypertrophic Cardiomyopathy Patients by Whole Exome Sequencingunc-94 encodes a tropomodulin in Caenorhabditis elegans.Isoform diversity of giant proteins in relation to passive and active contractile properties of rabbit skeletal muscles.Nebulin interacts with CapZ and regulates thin filament architecture within the Z-discApproximate model of cooperative activation and crossbridge cycling in cardiac muscle using ordinary differential equations.Sarcomeric actin organization is synergistically promoted by tropomodulin, ADF/cofilin, AIP1 and profilin in C. elegansA myopathy-linked desmin mutation perturbs striated muscle actin filament architecture.Reduced thin filament length in nebulin-knockout skeletal muscle alters isometric contractile propertiesThin filament length regulation in striated muscle sarcomeres: pointed-end dynamics go beyond a nebulin ruler.Designing heart performance by gene transfer.Thick and thin filament gene mutations in striated muscle diseases.Lifting the nebula: novel insights into skeletal muscle contractility.Clenbuterol plus granulocyte colony-stimulating factor regulates stem/progenitor cell mobilization and exerts beneficial effect by increasing neovascularization in rats with heart failure.Does Nebulin Make Tropomyosin Less Dynamic in Mature Myofibrils in Cross-Striated Myocytes?Titin and Nebulin in Thick and Thin Filament Length Regulation.Myofilaments: Movers and Rulers of the Sarcomere.Disorder profile of nebulin encodes a vernierlike position sensor for the sliding thin and thick filaments of the skeletal muscle sarcomere.Thin filament length in the cardiac sarcomere varies with sarcomere length but is independent of titin and nebulin.Leiomodin-2 is an antagonist of tropomodulin-1 at the pointed end of the thin filaments in cardiac muscle.Analysis of biophysical and functional consequences of tropomyosin-fluorescent protein fusions.The nebulin repeat protein Lasp regulates I-band architecture and filament spacing in myofibrils.UNC-87, a calponin-related protein in C. elegans, antagonizes ADF/cofilin-mediated actin filament dynamics.
P2860
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P2860
Nebulin regulates the assembly and lengths of the thin filaments in striated muscle
description
2005 nî lūn-bûn
@nan
2005年の論文
@ja
2005年学术文章
@wuu
2005年学术文章
@zh-cn
2005年学术文章
@zh-hans
2005年学术文章
@zh-my
2005年学术文章
@zh-sg
2005年學術文章
@yue
2005年學術文章
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2005年學術文章
@zh-hant
name
Nebulin regulates the assembly and lengths of the thin filaments in striated muscle
@ast
Nebulin regulates the assembly and lengths of the thin filaments in striated muscle
@en
type
label
Nebulin regulates the assembly and lengths of the thin filaments in striated muscle
@ast
Nebulin regulates the assembly and lengths of the thin filaments in striated muscle
@en
prefLabel
Nebulin regulates the assembly and lengths of the thin filaments in striated muscle
@ast
Nebulin regulates the assembly and lengths of the thin filaments in striated muscle
@en
P2093
P2860
P356
P1476
Nebulin regulates the assembly and lengths of the thin filaments in striated muscle
@en
P2093
Abigail S McElhinny
Carol C Gregorio
Catherine Schwach
Melinda Valichnac
Sarah Mount-Patrick
P2860
P304
P356
10.1083/JCB.200502158
P407
P577
2005-09-01T00:00:00Z