Schwann cell myelination requires timely and precise targeting of P(0) protein
about
P0 (protein zero) mutation S34C underlies instability of internodal myelin in S63C mice.Membrane traffic in myelinating oligodendrocytes.Myelinated nerve bundles developed on the plano-concave fibers containing nerve conduit.Proteolipid protein cannot replace P0 protein as the major structural protein of peripheral nervous system myelin.Comparison of a new pmp22 transgenic mouse line with other mouse models and human patients with CMT1A.P0S63del impedes the arrival of wild-type P0 glycoprotein to myelin in CMT1B mice.Renal collecting system growth and function depend upon embryonic γ1 laminin expression.MLCK regulates Schwann cell cytoskeletal organization, differentiation and myelination.Evolution of a neuroprotective function of central nervous system myelin.Epitope-tagged P(0) glycoprotein causes Charcot-Marie-Tooth-like neuropathy in transgenic mice.Pathomechanisms of mutant proteins in Charcot-Marie-Tooth disease.Proteolipid protein modulates preservation of peripheral axons and premature death when myelin protein zero is lacking.P0 protein is required for and can induce formation of schmidt-lantermann incisures in myelin internodesMpzR98C arrests Schwann cell development in a mouse model of early-onset Charcot-Marie-Tooth disease type 1B.Pathology of a mouse mutation in peripheral myelin protein P0 is characteristic of a severe and early onset form of human Charcot-Marie-Tooth type 1B disorder.P(0) glycoprotein overexpression causes congenital hypomyelination of peripheral nerves.Ablation of the UPR-mediator CHOP restores motor function and reduces demyelination in Charcot-Marie-Tooth 1B mice.A dual role for Integrin α6β4 in modulating Hereditary Neuropathy with liability to Pressure Palsies.Impairment of protein degradation and proteasome function in hereditary neuropathies.DHTKD1 deficiency causes Charcot-Marie-Tooth disease in mice.Knockout of p75(NTR) impairs re-myelination of injured sciatic nerve in mice.
P2860
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P2860
Schwann cell myelination requires timely and precise targeting of P(0) protein
description
2000 nî lūn-bûn
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2000年の論文
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2000年学术文章
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2000年学术文章
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2000年学术文章
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name
Schwann cell myelination requires timely and precise targeting of P(0) protein
@ast
Schwann cell myelination requires timely and precise targeting of P(0) protein
@en
type
label
Schwann cell myelination requires timely and precise targeting of P(0) protein
@ast
Schwann cell myelination requires timely and precise targeting of P(0) protein
@en
prefLabel
Schwann cell myelination requires timely and precise targeting of P(0) protein
@ast
Schwann cell myelination requires timely and precise targeting of P(0) protein
@en
P2093
P2860
P356
P1476
Schwann cell myelination requires timely and precise targeting of P(0) protein
@en
P2093
P2860
P304
P356
10.1083/JCB.148.5.1009
P407
P577
2000-03-01T00:00:00Z