Jagged 1 Rescues the Duchenne Muscular Dystrophy Phenotype.
about
Recent advances in innovative therapeutic approaches for Duchenne muscular dystrophy: from discovery to clinical trialsA POGLUT1 mutation causes a muscular dystrophy with reduced Notch signaling and satellite cell loss.Consequences of MEGF10 deficiency on myoblast function and Notch1 interactions.Report on the 3rd Ottawa International Conference on Neuromuscular Biology, Disease and Therapy - September 24-26, 2015, Ottawa, Canada.Notch ligands regulate the muscle stem-like state ex vivo but are not sufficient for retaining regenerative capacity.The golden retriever model of Duchenne muscular dystrophy.Satellite Cells in Muscular Dystrophy - Lost in Polarity.Molecular circuitry of stem cell fate in skeletal muscle regeneration, ageing and disease.Delta-Like Ligand 4 Modulates Liver Damage by Down-Regulating Chemokine Expression.Neuromuscular disorders: genes, genetic counseling and therapeutic trialsMuscle contraction is required to maintain the pool of muscle progenitors via YAP and NOTCH during fetal myogenesis.Stage-specific effects of Notch activation during skeletal myogenesis.Mass spectrometry-based protein analysis to unravel the tissue pathophysiology in Duchenne muscular dystrophy.Mechanisms of suppression: The wiring of genetic resilience.Roles of Notch1 Signaling in Regulating Satellite Cell Fates Choices and Postnatal Skeletal Myogenesis.Outside in: The matrix as a modifier of muscular dystrophy.Redox Control of Skeletal Muscle Regeneration.Long-term microdystrophin gene therapy is effective in a canine model of Duchenne muscular dystrophy.Dystrophin: The dead calm of a dogma.Deletion of Pofut1 in Mouse Skeletal Myofibers Induces Muscle Aging-Related Phenotypes in cis and in trans.Analysis of 589,306 genomes identifies individuals resilient to severe Mendelian childhood diseases.Repression of phosphatidylinositol transfer protein α ameliorates the pathology of Duchenne muscular dystrophy.Probing the Pathogenesis of Duchenne Muscular Dystrophy Using Mouse Models.Notch Signaling in Development, Tissue Homeostasis, and Disease.Interleukin-1beta (IL-1β)-induced Notch ligand Jagged1 suppresses mitogenic action of IL-1β on human dystrophic myogenic cells.Genetic modifiers of Duchenne and facioscapulohumeral muscular dystrophies.Methylmercury exposure causes a persistent inhibition of myogenin expression and C2C12 myoblast differentiation.Notch1 and Notch2 Coordinately Regulate Stem Cell Function in the Quiescent and Activated States of Muscle Satellite Cells.Immunoglobulin therapy ameliorates the phenotype and increases lifespan in the severely affected dystrophin-utrophin double knockout mice.Genetic profile of Brazilian patients with dystrophinopathies.Expression profiling of disease progression in canine model of Duchenne muscular dystrophy.Transplantation of Human Adipose Mesenchymal Stem Cells in Non-Immunosuppressed GRMD Dogs is a Safe Procedure.[Cell-autonomous defects in satellite cells impair muscle regeneration in Duchenne muscular dystrophy].Zidovudine ameliorates pathology in the mouse model of Duchenne muscular dystrophy via P2RX7 purinoceptor antagonism.A novel canine model for Duchenne muscular dystrophy (DMD): single nucleotide deletion in DMD gene exon 20.Changes in Muscle Metabolism are Associated with Phenotypic Variability in Golden Retriever Muscular Dystrophy.Targeting muscle stem cell intrinsic defects to treat Duchenne muscular dystrophy.Map of synthetic rescue interactions for the Fanconi anemia DNA repair pathway identifies USP48.At the Crossroads of Clinical and Preclinical Research for Muscular Dystrophy-Are We Closer to Effective Treatment for Patients?Krogh's principle for musculoskeletal physiology and pathology
P2860
Q26741409-34EF75D5-14EB-4342-896D-B7DCF20659E7Q29347528-61AF79F8-9FC0-4757-998F-73747BB6E964Q30274553-483BD34A-15CD-4E10-A5C1-3C152CD948AAQ30355125-672E868E-DC6E-4394-86C2-AF6AA1625822Q33674792-39B07E28-BD71-4999-95C8-1F388238E022Q33709114-F185A83C-2E7D-4E14-BC32-C57C6398C89AQ36948468-6655E428-E731-4139-B51A-72FD019F09EEQ37033031-F8E3E16D-F743-4D24-B1F9-6B3D3AA30F20Q37057161-58A104D0-6475-4CFC-AC32-403F102B22EAQ37217303-24A6F68C-711A-4A02-B2DD-3DCFE0F25FCEQ37270346-6E8F0054-E5B8-4682-9FA7-98A9B47BA40AQ37351564-6BDD88E0-CA15-4FFA-8433-82A79A758AC8Q38717697-6C69505C-86EF-4BB2-B6A1-C43F38E37EE9Q38743147-1BA24B85-520D-4751-83D9-7086E7DD5363Q39036264-485541E2-8625-4736-ACB3-6B6F4DCB7248Q39052032-19607E94-65D5-4DEC-97A5-38DF8739480FQ39059046-CF094017-1909-413F-B6B2-8075CB504AB5Q40109350-86F8B37B-FD8B-4D86-9D70-D2716A43C8C6Q40401861-20A9CA6B-4612-4CCF-ADEB-FC6D1E4C96A7Q42987220-6A77CE9F-3356-422C-A5D9-8A6D52ED9AEFQ44523764-B614408B-8D87-4FB5-9365-6D4FF13D536EQ45781418-C00653DD-9A05-4738-871A-A943D0162EB8Q45967109-2644D34B-7AD0-4356-AFB7-FB0E649CEF08Q46795621-41DCA50E-3285-4889-B7B4-16B4B324B524Q47148629-D93CB2E8-53D2-4602-98DC-0644FCA73112Q47337769-0FA01F5A-87F7-44BA-AB39-34D97AD5317EQ47440082-62938FE6-B60D-4AB2-8869-625C70472C1AQ48302103-6550D95A-3556-4259-A578-C7C1EC609B6CQ49644555-A3045BE8-0C95-4C84-9070-2D8C256DDC37Q51172109-ACA5C3C0-11EA-4CDA-ABBD-30F07FBC0180Q52648781-5B6C684D-B9BA-44E0-A7D5-CFDFA1EBA50FQ53097033-CBC1D65E-DC44-4898-80A5-7F6AE2A1F02BQ53842201-727C0AFD-FEE3-40A3-8533-6510EE48DFF2Q54116477-EA0B24D4-8657-481A-BD69-84A5BAFCBD71Q54977823-B5B639F7-0BF8-46C6-B298-D98D3C5051A2Q54988224-1497A4FB-C228-4929-BD81-D50FF178E706Q55063443-DEDA6E2F-142D-41D6-899F-16E87A2E7407Q55205670-F97993CA-EF69-44DF-B4D6-8CA9A1457E6BQ55361250-7D1ECF2B-FECA-4686-8859-00EE7A8ECA1BQ58774451-CF86A1E5-DE2F-489E-84AD-7EDAE50C4288
P2860
Jagged 1 Rescues the Duchenne Muscular Dystrophy Phenotype.
description
2015 nî lūn-bûn
@nan
2015年の論文
@ja
2015年学术文章
@wuu
2015年学术文章
@zh-cn
2015年学术文章
@zh-hans
2015年学术文章
@zh-my
2015年学术文章
@zh-sg
2015年學術文章
@yue
2015年學術文章
@zh
2015年學術文章
@zh-hant
name
Jagged 1 Rescues the Duchenne Muscular Dystrophy Phenotype.
@ast
Jagged 1 Rescues the Duchenne Muscular Dystrophy Phenotype.
@en
type
label
Jagged 1 Rescues the Duchenne Muscular Dystrophy Phenotype.
@ast
Jagged 1 Rescues the Duchenne Muscular Dystrophy Phenotype.
@en
prefLabel
Jagged 1 Rescues the Duchenne Muscular Dystrophy Phenotype.
@ast
Jagged 1 Rescues the Duchenne Muscular Dystrophy Phenotype.
@en
P2093
P2860
P50
P1433
P1476
Jagged 1 Rescues the Duchenne Muscular Dystrophy Phenotype.
@en
P2093
Ingegerd Elvers
Jamie L Marshall
Juliana P Gomes
Louis M Kunkel
Matthew S Alexander
Natassia M Vieira
Yuri B Moreira
P2860
P304
P356
10.1016/J.CELL.2015.10.049
P407
P577
2015-11-11T00:00:00Z