Protease-resistant modified human β-hexosaminidase B ameliorates symptoms in GM2 gangliosidosis model
about
MALDI imaging delineates hippocampal glycosphingolipid changes associated with neurotoxin induced proteopathy following neonatal BMAA exposure.Chronic Enzyme Replacement to the Brain of a Late Infantile Neuronal Ceroid Lipofuscinosis Mouse Has Differential Effects on Phenotypes of Disease.Crystal structure of native β-N-acetylhexosaminidase isolated from Aspergillus oryzae sheds light onto its substrate specificity, high stability, and regulation by propeptide.Neuronal pentraxin 1 depletion delays neurodegeneration and extends life in Sandhoff disease mice.
P2860
Protease-resistant modified human β-hexosaminidase B ameliorates symptoms in GM2 gangliosidosis model
description
2016 nî lūn-bûn
@nan
2016年の論文
@ja
2016年論文
@yue
2016年論文
@zh-hant
2016年論文
@zh-hk
2016年論文
@zh-mo
2016年論文
@zh-tw
2016年论文
@wuu
2016年论文
@zh
2016年论文
@zh-cn
name
Protease-resistant modified hu ...... ms in GM2 gangliosidosis model
@en
type
label
Protease-resistant modified hu ...... ms in GM2 gangliosidosis model
@en
prefLabel
Protease-resistant modified hu ...... ms in GM2 gangliosidosis model
@en
P2093
P2860
P356
P1476
Protease-resistant modified hu ...... ms in GM2 gangliosidosis model
@en
P2093
Akira Otaka
Chikako Tasaki
Daisuke Asanuma
Daisuke Tsuji
Eiji Sugiyama
Hitoshi Sakuraba
Kohei Sato
Kohji Itoh
Mako Kamiya
Mitsutoshi Setou
P2860
P304
P356
10.1172/JCI85300
P407
P577
2016-03-28T00:00:00Z