Dystrophic skeletal muscle fibers display alterations at the level of calcium microdomains.
about
Alternating bipolar field stimulation identifies muscle fibers with defective excitability but maintained local Ca(2+) signals and contraction.Absence of physiological Ca2+ transients is an initial trigger for mitochondrial dysfunction in skeletal muscle following denervation.DNA transfection of mammalian skeletal muscles using in vivo electroporation.Hyperactive intracellular calcium signaling associated with localized mitochondrial defects in skeletal muscle of an animal model of amyotrophic lateral sclerosisMicroarchitecture is severely compromised but motor protein function is preserved in dystrophic mdx skeletal muscle.Effects of chronic administration of clenbuterol on contractile properties and calcium homeostasis in rat extensor digitorum longus muscle.Excitation-contraction coupling alterations in mdx and utrophin/dystrophin double knockout mice: a comparative study.Action potential-evoked calcium release is impaired in single skeletal muscle fibers from heart failure patients.Mitigation of muscular dystrophy in mice by SERCA overexpression in skeletal muscle.Mitochondrial calcium uptake regulates rapid calcium transients in skeletal muscle during excitation-contraction (E-C) coupling.Sarcoplasmic reticulum Ca2+ permeation explored from the lumen side in mdx muscle fibers under voltage controlEarly metabolic changes measured by 1H MRS in healthy and dystrophic muscle after injuryNanospan, an alternatively spliced isoform of sarcospan, localizes to the sarcoplasmic reticulum in skeletal muscle and is absent in limb girdle muscular dystrophy 2F.Attenuated Ca(2+) release in a mouse model of limb girdle muscular dystrophy 2A.Low-affinity Ca2+ indicators compared in measurements of skeletal muscle Ca2+ transients.Myofibrillar misalignment correlated to triad disappearance of mdx mouse gastrocnemius muscle probed by SHG microscopy.Mitochondrial Ca(2+) uptake in skeletal muscle health and disease.Leaky ryanodine receptors in β-sarcoglycan deficient mice: a potential common defect in muscular dystrophy.
P2860
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P2860
Dystrophic skeletal muscle fibers display alterations at the level of calcium microdomains.
description
2008 nî lūn-bûn
@nan
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
2008年论文
@zh
2008年论文
@zh-cn
name
Dystrophic skeletal muscle fib ...... level of calcium microdomains.
@en
type
label
Dystrophic skeletal muscle fib ...... level of calcium microdomains.
@en
prefLabel
Dystrophic skeletal muscle fib ...... level of calcium microdomains.
@en
P2093
P2860
P356
P1476
Dystrophic skeletal muscle fib ...... level of calcium microdomains.
@en
P2093
Christopher E Woods
Joana Capote
Julio L Vergara
Marino DiFranco
P2860
P304
14698-14703
P356
10.1073/PNAS.0802217105
P407
P577
2008-09-11T00:00:00Z