Characterization of truncated forms of abnormal prion protein in Creutzfeldt-Jakob disease.
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Detection of prion protein in urine-derived injectable fertility products by a targeted proteomic approachAnalysis of Conformational Stability of Abnormal Prion Protein Aggregates across the Spectrum of Creutzfeldt-Jakob Disease PrionsHuman prion diseases in the Netherlands (1998-2009): clinical, genetic and molecular aspects.Prion protein amyloidosis with divergent phenotype associated with two novel nonsense mutations in PRNP.Biochemical characterization of prion strains in bank volesMultiorgan detection and characterization of protease-resistant prion protein in a case of variant CJD examined in the United States.Prions of ruminants show distinct splenotropisms in an ovine transgenic mouse model.Protease-sensitive conformers in broad spectrum of distinct PrPSc structures in sporadic Creutzfeldt-Jakob disease are indicator of progression rate.Characterization of the prion protein in human urine.Concurrent variably protease-sensitive prionopathy and amyotrophic lateral sclerosis.Regional distribution of anchorless prion protein, PrP226*, in the human brainA novel seven-octapeptide repeat insertion in the prion protein gene (PRNP) in a Dutch pedigree with Gerstmann-Sträussler-Scheinker disease phenotype: comparison with similar cases from the literature.Structural organization of mammalian prions as probed by limited proteolysis.Comparative Study of Prions in Iatrogenic and Sporadic Creutzfeldt-Jakob Disease.Molecular biology and pathology of prion strains in sporadic human prion diseases.Detection of the GPI-anchorless prion protein fragment PrP226* in human brain.Human PrP90-231-induced cell death is associated with intracellular accumulation of insoluble and protease-resistant macroaggregates and lysosomal dysfunction.Fibril formation of the rabbit/human/bovine prion proteinsMolecular typing of protease-resistant prion protein in transmissible spongiform encephalopathies of small ruminants, France, 2002-2009Assessing prion infectivity of human urine in sporadic Creutzfeldt-Jakob diseaseIntegrity of helix 2-helix 3 domain of the PrP protein is not mandatory for prion replication.Molecular pathogenesis of sporadic prion diseases in man.Consensus classification of human prion disease histotypes allows reliable identification of molecular subtypes: an inter-rater study among surveillance centres in Europe and USAAnalyses of protease resistance and aggregation state of abnormal prion protein across the spectrum of human prionsIncidence and spectrum of sporadic Creutzfeldt-Jakob disease variants with mixed phenotype and co-occurrence of PrPSc types: an updated classificationCrowded cell-like environment accelerates the nucleation step of amyloidogenic protein misfolding.Prion protein misfolding, strains, and neurotoxicity: an update from studies on Mammalian prions.Novel strain properties distinguishing sporadic prion diseases sharing prion protein genotype and prion type.Gerstmann-Sträussler-Scheinker disease and "anchorless prion protein" mice share prion conformational properties diverging from sporadic Creutzfeldt-Jakob disease.Biochemical and strain properties of CJD prions: complexity versus simplicity.TSE diagnostics: recent advances in immunoassaying prions.Different Molecular Mechanisms Mediate Direct or Glia-Dependent Prion Protein Fragment 90-231 Neurotoxic Effects in Cerebellar Granule Neurons.Role of ADAMs in the ectodomain shedding and conformational conversion of the prion protein.Foodborne transmission of bovine spongiform encephalopathy to nonhuman primates.Atypical Creutzfeldt-Jakob disease with PrP-amyloid plaques in white matter: molecular characterization and transmission to bank voles show the M1 strain signature.Prion Proteins Without the Glycophosphatidylinositol Anchor: Potential Biomarkers in Neurodegenerative Diseases.
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P2860
Characterization of truncated forms of abnormal prion protein in Creutzfeldt-Jakob disease.
description
article científic
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article scientifique
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articolo scientifico
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artigo científico
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bilimsel makale
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scientific article published on 27 August 2008
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vedecký článok
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vetenskaplig artikel
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videnskabelig artikel
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vědecký článek
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name
Characterization of truncated ...... in Creutzfeldt-Jakob disease.
@en
Characterization of truncated ...... in Creutzfeldt-Jakob disease.
@nl
type
label
Characterization of truncated ...... in Creutzfeldt-Jakob disease.
@en
Characterization of truncated ...... in Creutzfeldt-Jakob disease.
@nl
prefLabel
Characterization of truncated ...... in Creutzfeldt-Jakob disease.
@en
Characterization of truncated ...... in Creutzfeldt-Jakob disease.
@nl
P2093
P2860
P356
P1476
Characterization of truncated ...... in Creutzfeldt-Jakob disease.
@en
P2093
Bernardino Ghetti
Hans A Kretzschmar
Jacques Grassi
Jan P M Langeveld
Maura Cescatti
Pierluigi Gambetti
Rosaria Strammiello
Sabina Capellari
Silvio Notari
Wen-Quan Zou
P2860
P304
30557-30565
P356
10.1074/JBC.M801877200
P407
P577
2008-08-27T00:00:00Z