Ivacaftor treatment of cystic fibrosis patients with the G551D mutation: a review of the evidence.
about
A survey of detergents for the purification of stable, active human cystic fibrosis transmembrane conductance regulator (CFTR).Potentiator ivacaftor abrogates pharmacological correction of ΔF508 CFTR in cystic fibrosis.PharmGKB summary: very important pharmacogene information for CFTRAlterations in blood leukocytes of G551D-bearing cystic fibrosis patients undergoing treatment with ivacaftor.Functional defect of variants in the adenosine triphosphate-binding sites of ABCB4 and their rescue by the cystic fibrosis transmembrane conductance regulator potentiator, ivacaftor (VX-770).Mutation spectrum of Egyptian children with cystic fibrosis.Genetic, cell biological, and clinical interrogation of the CFTR mutation c.3700 A>G (p.Ile1234Val) informs strategies for future medical intervention.Mesenchymal Stem Cell Soluble Mediators and Cystic Fibrosis.Nasospheroids permit measurements of CFTR-dependent fluid transport.Ataluren for the treatment of cystic fibrosis.
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P2860
Ivacaftor treatment of cystic fibrosis patients with the G551D mutation: a review of the evidence.
description
article científic
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article scientifique
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articol științific
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articolo scientifico
@it
artigo científico
@gl
artigo científico
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artigo científico
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artikel ilmiah
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artikull shkencor
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artículo científico
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name
Ivacaftor treatment of cystic ...... ion: a review of the evidence.
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type
label
Ivacaftor treatment of cystic ...... ion: a review of the evidence.
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prefLabel
Ivacaftor treatment of cystic ...... ion: a review of the evidence.
@en
P2860
P356
P1476
Ivacaftor treatment of cystic ...... ion: a review of the evidence.
@en
P2093
John P Clancy
Kavitha Kotha
P2860
P304
P356
10.1177/1753465813502115
P577
2013-09-03T00:00:00Z