Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.
about
The Role of the Heat Shock Protein B8 (HSPB8) in Motoneuron Diseases.Endoplasmic Reticulum Malfunction in the Nervous System.A novel splice variant in EMC1 is associated with cerebellar atrophy, visual impairment, psychomotor retardation with epilepsy.Activating transcription factor 6α deficiency exacerbates oligodendrocyte death and myelin damage in immune-mediated demyelinating diseases.EIF2B2 mutations in Vanishing White Matter Disease hyper- suppress translation and delay recovery during the integrated stress response.Myelin protein zero mutations and the unfolded protein response in Charcot Marie Tooth disease type 1B.Efficacy of exogenous pyruvate in Trembler mouse model of Charcot-Marie-Tooth neuropathy
P2860
Q33819258-6006E117-86EE-4DCB-83DE-1CDC3846E6C0Q42290598-38C1CD7F-8E74-4C0E-9FEE-4DFA7E01B43EQ47260968-6EA428A9-0C0C-4BD5-820A-159A5967E70AQ50050062-4DDE49BA-FAFC-41F5-95DD-4C3E6561E7C5Q52327584-09E6F73C-8055-446C-ABE9-A4EACD32409CQ52717186-108726BC-3AFC-493D-89F1-C40F419934A8Q58702974-3AB900EB-6603-4FA7-8B64-A2149C511687
P2860
Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.
description
2016 nî lūn-bûn
@nan
2016 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2016年の論文
@ja
2016年論文
@yue
2016年論文
@zh-hant
2016年論文
@zh-hk
2016年論文
@zh-mo
2016年論文
@zh-tw
2016年论文
@wuu
2016年论文
@zh
name
Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.
@en
Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.
@nl
type
label
Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.
@en
Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.
@nl
prefLabel
Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.
@en
Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.
@nl
P2860
P356
P1476
Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.
@en
P2093
Maurizio D'Antonio
Vera G Volpi
P2860
P356
10.3389/FNMOL.2016.00162
P577
2016-01-01T00:00:00Z