CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.

CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.

Item
http://www.wikidata.org/entity/Q39232101
microRNA-mediated differential expression of TRMU, GTPBP3 and MTO1 in cell models of mitochondrial-DNA diseases.Autophagy compensates impaired energy metabolism in CLPXP-deficient Podospora anserina strains and extends healthspan.A homozygous missense mutation in ERAL1, encoding a mitochondrial rRNA chaperone, causes Perrault syndrome.Genetic diagnosis of Mendelian disorders via RNA sequencing.Drosophila protease ClpXP specifically degrades DmLRPPRC1 controlling mitochondrial mRNA and translation.Primary Ovarian Insufficiency and Azospermia in Carriers of a Homozygous PSMC3IP Stop Gain Mutation.Defects in the mitochondrial-tRNA modification enzymes MTO1 and GTPBP3 promote different metabolic reprogramming through a HIF-PPARγ-UCP2-AMPK axis.Loss of mitochondrial protease ClpP protects mice from diet-induced obesity and insulin resistance.Role of LTBP4 in alveolarization, angiogenesis, and fibrosis in lungs.CLPP deficiency protects against metabolic syndrome but hinders adaptive thermogenesis.DNA Checkpoint and Repair Factors Are Nuclear Sensors for Intracellular Organelle Stresses-Inflammations and Cancers Can Have High Genomic Risks.The mitochondrial unfolded protein response and mitohormesis: a perspective on metabolic diseasesPerrault syndrome type 3 caused by diverse molecular defects in CLPPLon protease inactivation in causes unfolded protein stress and inhibition of mitochondrial translation
P2860

CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.

Item
http://www.wikidata.org/entity/Q39232101
description
2016 nî lūn-bûn
@nan
2016年の論文
@ja
2016年論文
@yue
2016年論文
@zh-hant
2016年論文
@zh-hk
2016年論文
@zh-mo
2016年論文
@zh-tw
2016年论文
@wuu
2016年论文
@zh
2016年论文
@zh-cn
name
CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.
@en
CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.
@nl
type
label
CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.
@en
CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.
@nl
prefLabel
CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.
@en
CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.
@nl
P1433
P1476
P2093
P2860
P304
P31
P356
P407
P433
P478
P50
P577
P698
P932
P356
P1433
P1476
CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels
@en
P2093
P2860
P304
P31
P356
P407
P433
P478
P50
P577
P698
P932