[Light and electron microscopic liver changes in the cerebro-hepato-renal syndrome of Zellweger (Peroxisome deficiency) (author's transl)]
about
Carbohydrate metabolism is perturbed in peroxisome-deficient hepatocytes due to mitochondrial dysfunction, AMP-activated protein kinase (AMPK) activation, and peroxisome proliferator-activated receptor γ coactivator 1α (PGC-1α) suppression.Criteria for development of animal models of diseases of the gastrointestinal system.Ultrastructural and cytochemical demonstration of peroxisomes in cultured fibroblasts from patients with peroxisomal deficiency disorders.Lignoceric acid is oxidized in the peroxisome: implications for the Zellweger cerebro-hepato-renal syndrome and adrenoleukodystrophy.Peroxisomal organization in normal and cerebrohepatorenal (Zellweger) syndrome fibroblasts.Zellweger syndrome: a histochemical diagnosis of two cases.Ultrastructure of the liver in th cerebrohepatorenal syndrome of Zellweger.Angulate lysosomes.
P2860
Q35604967-500B303C-AA0C-4FFB-871D-A0554020FAD5Q35863517-4D513050-8821-4E2B-B11A-6ABD91CF569DQ36213312-18335AB8-FC34-49DF-8D69-9DE8614FEDA2Q36265198-B8CEE71A-C962-4629-83CC-C018E02532F7Q37550462-6A88737D-E03D-4B6D-8E12-719D50CDB774Q45222864-DE31D574-0A96-4A79-AD31-1B72A688F312Q48750346-32DBD748-CC62-4208-92CA-94F18D93C474Q48753410-B3945174-83EC-409F-BF78-938753905C82
P2860
[Light and electron microscopic liver changes in the cerebro-hepato-renal syndrome of Zellweger (Peroxisome deficiency) (author's transl)]
description
1979 nî lūn-bûn
@nan
1979年の論文
@ja
1979年学术文章
@wuu
1979年学术文章
@zh-cn
1979年学术文章
@zh-hans
1979年学术文章
@zh-my
1979年学术文章
@zh-sg
1979年學術文章
@yue
1979年學術文章
@zh
1979年學術文章
@zh-hant
name
[Light and electron microscopi ...... deficiency) (author's transl)]
@en
[Light and electron microscopi ...... to-renal syndrome of Zellweger
@nl
type
label
[Light and electron microscopi ...... deficiency) (author's transl)]
@en
[Light and electron microscopi ...... to-renal syndrome of Zellweger
@nl
prefLabel
[Light and electron microscopi ...... deficiency) (author's transl)]
@en
[Light and electron microscopi ...... to-renal syndrome of Zellweger
@nl
P356
P1476
[Light and electron microscopi ...... deficiency) (author's transl)]
@en
P2093
P304
P356
10.1007/BF00428229
P577
1979-10-01T00:00:00Z