Two endoplasmic reticulum-associated degradation (ERAD) systems for the novel variant of the mutant dysferlin: ubiquitin/proteasome ERAD(I) and autophagy/lysosome ERAD(II). - Wikidata - wikimedia - TriplyDB

Two endoplasmic reticulum-associated degradation (ERAD) systems for the novel variant of the mutant dysferlin: ubiquitin/proteasome ERAD(I) and autophagy/lysosome ERAD(II).

Two endoplasmic reticulum-associated degradation (ERAD) systems for the novel variant of the mutant dysferlin: ubiquitin/proteasome ERAD(I) and autophagy/lysosome ERAD(II).

http://www.wikidata.org/entity/Q40164655

about

Guidelines for the use and interpretation of assays for monitoring autophagy Nrf2 and Nrf1 signaling and ER stress crosstalk: implication for proteasomal degradation and autophagy Mpl traffics to the cell surface through conventional and unconventional routes Reduced plasma membrane expression of dysferlin mutants is attributed to accelerated endocytosis via a syntaxin-4-associated pathway XBP-1 deficiency in the nervous system protects against amyotrophic lateral sclerosis by increasing autophagy The beneficial role of proteolysis in skeletal muscle growth and stress adaptation Endoplasmic Reticulum Stress in the Diabetic Kidney, the Good, the Bad and the Ugly Protein folding and quality control in the ER Mechanisms for quality control of misfolded transmembrane proteins The delicate balance between secreted protein folding and endoplasmic reticulum-associated degradation in human physiology Autophagy in plasma cell pathophysiology Autophagy attenuates diabetic glomerular damage through protection of hyperglycemia-induced podocyte injury Dysferlin-peptides reallocate mutated dysferlin thereby restoring function A pro-cathepsin L mutant is a luminal substrate for endoplasmic-reticulum-associated degradation in C. elegans Perturbation of autophagic pathway by hepatitis C virus Arms Race between Enveloped Viruses and the Host ERAD Machinery The divergent roles of autophagy in ischemia and preconditioning Inflammation and cellular stress: a mechanistic link between immune-mediated and metabolically driven pathologies Knockdown of PSMB7 induces autophagy in cardiomyocyte cultures: possible role in endoplasmic reticulum stress 2-Hydroxyoleic acid induces ER stress and autophagy in various human glioma cell lines Critical significance of the region between Helix 1 and 2 for efficient dominant-negative inhibition by conversion-incompetent prion protein FBG1 Is the Final Arbitrator of A1AT-Z Degradation The ER-associated degradation adaptor protein Sel1L regulates LPL secretion and lipid metabolism Regulation mechanisms and signaling pathways of autophagy Recessive mutations in EPG5 cause Vici syndrome, a multisystem disorder with defective autophagy.Enhanced lysosomal activity is involved in Bax inhibitor-1-induced regulation of the endoplasmic reticulum (ER) stress response and cell death against ER stress: involvement of vacuolar H+-ATPase (V-ATPase).Early Delivery of Misfolded PrP from ER to Lysosomes by Autophagy.A human carboxypeptidase E/NF-α1 gene mutation in an Alzheimer's disease patient leads to dementia and depression in mice.Autophagy and the ubiquitin-proteasome system in cardiac dysfunction.Proteomic analysis of the dysferlin protein complex unveils its importance for sarcolemmal maintenance and integrity Myogenic differentiation of VCP disease-induced pluripotent stem cells: A novel platform for drug discovery Quality control autophagy degrades soluble ERAD-resistant conformers of the misfolded membrane protein GnRHR The characteristics of Bax inhibitor-1 and its related diseases.Nonimmune mechanisms of muscle damage in myositis: role of the endoplasmic reticulum stress response and autophagy in the disease pathogenesis.ER stress, autophagy, and RNA viruses.Crohn's disease: NOD2, autophagy and ER stress converge.Activation of ERAD pathway by human hepatitis B virus modulates viral and subviral particle production.Therapeutic exon skipping for dysferlinopathies?Identification of the Drosophila ortholog of HSPB8: implication of HSPB8 loss of function in protein folding diseases.TNF-alpha induces macroautophagy and regulates MHC class II expression in human skeletal muscle cells.

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P2860

Two endoplasmic reticulum-associated degradation (ERAD) systems for the novel variant of the mutant dysferlin: ubiquitin/proteasome ERAD(I) and autophagy/lysosome ERAD(II).

http://www.wikidata.org/entity/Q40164655

description

2007 nî lūn-bûn

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2007年の論文

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2007年論文

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2007年論文

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2007年論文

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2007年論文

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2007年論文

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2007年论文

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2007年论文

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2007年论文

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name

Two endoplasmic reticulum-asso ...... d autophagy/lysosome ERAD(II).

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Two endoplasmic reticulum-asso ...... d autophagy/lysosome ERAD(II).

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Two endoplasmic reticulum-asso ...... d autophagy/lysosome ERAD(II).

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Human Molecular Genetics

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Two endoplasmic reticulum-asso ...... d autophagy/lysosome ERAD(II).

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P2093

Akifumi Misutani

http://www.w3.org/2001/XMLSchema#string

Atsushi Isoai

http://www.w3.org/2001/XMLSchema#string

Chie Matsuda

http://www.w3.org/2001/XMLSchema#string

Eriko Fujita

http://www.w3.org/2001/XMLSchema#string

Hiromichi Kumagai

http://www.w3.org/2001/XMLSchema#string

Takashi Momoi

http://www.w3.org/2001/XMLSchema#string

Yoriko Kouroku

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Yukiko K Hayashi

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P2860

Calcium-sensitive phospholipid binding properties of normal and mutant ferlin C2 domains

A membrane protein complex mediates retro-translocation from the ER lumen into the cytosol

Human light chain 3/MAP1LC3B is cleaved at its carboxyl-terminal Met121 to expose Gly120 for lipidation and targeting to autophagosomal membranes

Recruitment of the p97 ATPase and ubiquitin ligases to the site of retrotranslocation at the endoplasmic reticulum membrane

Beclin-phosphatidylinositol 3-kinase complex functions at the trans-Golgi network

Characterization of an ERAD gene as VPS30/ATG6 reveals two alternative and functionally distinct protein quality control pathways: one for soluble Z variant of human alpha-1 proteinase inhibitor (A1PiZ) and another for aggregates of A1PiZ.

In vivo analysis of autophagy in response to nutrient starvation using transgenic mice expressing a fluorescent autophagosome marker

Dissection of autophagosome formation using Apg5-deficient mouse embryonic stem cells

A new technique for the assay of infectivity of human adenovirus 5 DNA

TOR, a central controller of cell growth.

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618-629

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scholarly article

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10.1093/HMG/DDM002

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6

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P478

16

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2007-03-01T00:00:00Z

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6474658

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17331981

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ubiquitin-proteasome system

endoplasmic reticulum