Restoration of type VII collagen expression and function in dystrophic epidermolysis bullosa. - Wikidata - wikimedia - TriplyDB

Restoration of type VII collagen expression and function in dystrophic epidermolysis bullosa.

Restoration of type VII collagen expression and function in dystrophic epidermolysis bullosa.

http://www.wikidata.org/entity/Q40690917

about

Gene therapy for skin diseases One goal, different strategies--molecular and cellular approaches for the treatment of inherited skin fragility disorders Dystrophic epidermolysis bullosa: a review Mutation analysis and characterization of COL7A1 mutations in dystrophic epidermolysis bullosa Aminoglycosides restore full-length type VII collagen by overcoming premature termination codons: therapeutic implications for dystrophic epidermolysis bullosa.Positive selection, relaxation, and acceleration in the evolution of the human and chimp genome.In vivo stable transduction of humanized liver tissue in chimeric mice via high-capacity adenovirus-lentivirus hybrid vector.Injection of recombinant human type VII collagen corrects the disease phenotype in a murine model of dystrophic epidermolysis bullosa.Mechanisms of fibroblast cell therapy for dystrophic epidermolysis bullosa: high stability of collagen VII favors long-term skin integrity Induced pluripotent stem cells from individuals with recessive dystrophic epidermolysis bullosa.Bone marrow transplantation for recessive dystrophic epidermolysis bullosa Stem cells of the skin epithelium.Generation of keratinocytes from normal and recessive dystrophic epidermolysis bullosa-induced pluripotent stem cells.Human COL7A1-corrected induced pluripotent stem cells for the treatment of recessive dystrophic epidermolysis bullosa Dystrophic epidermolysis bullosa.Translational benefits from research on rare genodermatoses.Gene transfer to epidermal stem cells: implications for tissue engineering.Permanent, lowered HLA class I expression using lentivirus vectors with shRNA constructs: Averting cytotoxicity by alloreactive T lymphocytes.Gene therapy of epidermolysis bullosa.Vesicobullous disorders of female genitalia.Current approaches and perspectives in human keratinocyte-based gene therapies.Gene editing toward the use of autologous therapies in recessive dystrophic epidermolysis bullosa.Gene therapy in combination with tissue engineering to treat epidermolysis bullosa.Lentiviral Engineered Fibroblasts Expressing Codon-Optimized COL7A1 Restore Anchoring Fibrils in RDEB.Cutaneous gene therapy.Amelioration of epidermolysis bullosa by transfer of wild-type bone marrow cells An approach to achieve long-term expression in skin gene therapy.Allogeneic blood and bone marrow cells for the treatment of severe epidermolysis bullosa: repair of the extracellular matrix.Efficient in vivo gene editing using ribonucleoproteins in skin stem cells of recessive dystrophic epidermolysis bullosa mouse model.Novel and emerging therapies in the treatment of recessive dystrophic epidermolysis bullosa.Hox transcription factor regulation of adult bone-marrow-derived cell behaviour during tissue repair and regeneration.Concise review: Transplantation of human hematopoietic cells for extracellular matrix protein deficiency in epidermolysis bullosa.Lentiviral vectors for cutaneous RNA managing.Gene therapy: pursuing restoration of dermal adhesion in recessive dystrophic epidermolysis bullosa.De novo anti-type VII collagen antibodies in patients with recessive dystrophic epidermolysis bullosa.Characterization of factors that determine lentiviral vector tropism in skin tissue using an ex vivo model.Injection of genetically engineered fibroblasts corrects regenerated human epidermolysis bullosa skin tissue.Collagen alpha1(I) gene (COL1A1) is repressed by RFX family Gene transfer in human skin with different pseudotyped HIV-based vectors.SLY1 and Syntaxin 18 specify a distinct pathway for procollagen VII export from the endoplasmic reticulum.

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P2860

Restoration of type VII collagen expression and function in dystrophic epidermolysis bullosa.

http://www.wikidata.org/entity/Q40690917

description

2002 nî lūn-bûn

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2002年の論文

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2002年論文

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2002年論文

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2002年论文

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2002年论文

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name

Restoration of type VII collag ...... trophic epidermolysis bullosa.

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Restoration of type VII collag ...... trophic epidermolysis bullosa.

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Restoration of type VII collag ...... trophic epidermolysis bullosa.

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Nature Genetics

P1476

Restoration of type VII collag ...... trophic epidermolysis bullosa.

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P2093

Constance Mazurek

http://www.w3.org/2001/XMLSchema#string

David T Woodley

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Deborah Finlay

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Douglas R Keene

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Lawrence Chan

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Maria Barcova

http://www.w3.org/2001/XMLSchema#string

Mei Chen

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Noriyuki Kasahara

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Paula M Cannon

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Warren K Hoeffler

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P2860

In vivo assessment of gene delivery to keratinocytes by lentiviral vectors

Type VII collagen, anchoring fibrils, and epidermolysis bullosa.

Lentiviruses as gene transfer agents for delivery to non-dividing cells.

Consistent, persistent expression from modified retroviral vectors in murine hematopoietic stem cells.

Efficient transfer, integration, and sustained long-term expression of the transgene in adult rat brains injected with a lentiviral vector.

The recombinant expression of full-length type VII collagen and characterization of molecular mechanisms underlying dystrophic epidermolysis bullosa.

Molecular basis for the dystrophic forms of epidermolysis bullosa: mutations in the type VII collagen gene.

Titering lentiviral vectors: comparison of DNA, RNA and marker expression methods.

Spontaneous cell sorting of fibroblasts and keratinocytes creates an organotypic human skin equivalent.

The phagokinetic tracks of 3T3 cells.

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670-675

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10.1038/NG1041

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P433

4

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P478

32

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2002-11-11T00:00:00Z

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11039630

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1048985937

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12426566

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