The Fanconi syndrome of cystinosis: insights into the pathophysiology.
about
Decreased intracellular ATP content and intact mitochondrial energy generating capacity in human cystinotic fibroblastsAltered status of glutathione and its metabolites in cystinotic cellsCystinosis: a reviewCystinosis: the evolution of a treatable diseaseThe redox status of cystinotic fibroblasts.Dietary supplementation with essential amino acids boosts the beneficial effects of rosuvastatin on mouse kidneyProximal renal tubular acidosis: a not so rare disorder of multiple etiologiesCystinosis: a new perspective.The renal Fanconi syndrome in cystinosis: pathogenic insights and therapeutic perspectives.Mitochondrial complex V expression and activity in cystinotic fibroblasts.Impaired activity of the gamma-glutamyl cycle in nephropathic cystinosis fibroblasts.The reduced expression of proximal tubular transporters in acquired Fanconi syndrome with κ light chain deposition.Evaluation of the proximal tubular function in hereditary renal Fanconi syndrome.
P2860
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P2860
The Fanconi syndrome of cystinosis: insights into the pathophysiology.
description
1998 nî lūn-bûn
@nan
1998年の論文
@ja
1998年学术文章
@wuu
1998年学术文章
@zh-cn
1998年学术文章
@zh-hans
1998年学术文章
@zh-my
1998年学术文章
@zh-sg
1998年學術文章
@yue
1998年學術文章
@zh
1998年學術文章
@zh-hant
name
The Fanconi syndrome of cystinosis: insights into the pathophysiology.
@en
type
label
The Fanconi syndrome of cystinosis: insights into the pathophysiology.
@en
prefLabel
The Fanconi syndrome of cystinosis: insights into the pathophysiology.
@en
P356
P1433
P1476
The Fanconi syndrome of cystinosis: insights into the pathophysiology.
@en
P2093
P2888
P304
P356
10.1007/S004670050495
P577
1998-08-01T00:00:00Z
P6179
1009168903