The MitCHAP-60 disease is due to entropic destabilization of the human mitochondrial Hsp60 oligomer.
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Disease-Associated Mutations in the HSPD1 Gene Encoding the Large Subunit of the Mitochondrial HSP60/HSP10 Chaperonin ComplexHuman Hsp60 with its mitochondrial import signal occurs in solution as heptamers and tetradecamers remarkably stable over a wide range of concentrations.Identification of elements that dictate the specificity of mitochondrial Hsp60 for its co-chaperonin.Effects of a Mutation in the HSPE1 Gene Encoding the Mitochondrial Co-chaperonin HSP10 and Its Potential Association with a Neurological and Developmental Disorder.Barcoding heat shock proteins to human diseases: looking beyond the heat shock responseThe human mitochondrial Hsp60 in the APO conformation forms a stable tetradecameric complex.Crystallization and structure determination of a symmetrical 'football' complex of the mammalian mitochondrial Hsp60-Hsp10 chaperonins.HSP60 possesses a GTPase activity and mediates protein folding with HSP10.Frataxin-deficient neurons and mice models of Friedreich ataxia are improved by TAT-MTScs-FXN treatment.Chaperonin of Group I: Oligomeric Spectrum and Biochemical and Biological Implications.Toward Developing Chemical Modulators of Hsp60 as Potential Therapeutics.Single-Ring Intermediates Are Essential for Some Chaperonins.Quaternary structures of GroEL and naïve-Hsp60 chaperonins in solution: a combined SAXS-MD study
P2860
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P2860
The MitCHAP-60 disease is due to entropic destabilization of the human mitochondrial Hsp60 oligomer.
description
2009 nî lūn-bûn
@nan
2009年の論文
@ja
2009年論文
@yue
2009年論文
@zh-hant
2009年論文
@zh-hk
2009年論文
@zh-mo
2009年論文
@zh-tw
2009年论文
@wuu
2009年论文
@zh
2009年论文
@zh-cn
name
The MitCHAP-60 disease is due ...... mitochondrial Hsp60 oligomer.
@en
type
label
The MitCHAP-60 disease is due ...... mitochondrial Hsp60 oligomer.
@en
prefLabel
The MitCHAP-60 disease is due ...... mitochondrial Hsp60 oligomer.
@en
P2093
P2860
P356
P1476
The MitCHAP-60 disease is due ...... mitochondrial Hsp60 oligomer.
@en
P2093
Abdussalam Azem
Amnon Horovitz
Avital Parnas
Hanna Mandel
Michal Nadler
Shahar Nisemblat
P2860
P304
28198-28203
P356
10.1074/JBC.M109.031997
P407
P577
2009-08-25T00:00:00Z