Inflammation in Lafora Disease: Evolution with Disease Progression in Laforin and Malin Knock-out Mouse Models.

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Suppression of leptin signaling reduces polyglucosan inclusions and seizure susceptibility in a mouse model for Lafora disease.Astrocytes: new players in progressive myoclonus epilepsy of Lafora type.

P2860

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Inflammation in Lafora Disease: Evolution with Disease Progression in Laforin and Malin Knock-out Mouse Models.

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http://www.wikidata.org/entity/Q41886528

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2016 nî lūn-bûn

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2016年の論文

@ja

2016年論文

@yue

2016年論文

@zh-hant

2016年論文

@zh-hk

2016年論文

@zh-mo

2016年論文

@zh-tw

2016年论文

@wuu

2016年论文

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2016年论文

@zh-cn

name

Inflammation in Lafora Disease ...... Malin Knock-out Mouse Models.

@en

type

Item

label

Inflammation in Lafora Disease ...... Malin Knock-out Mouse Models.

@en

prefLabel

Inflammation in Lafora Disease ...... Malin Knock-out Mouse Models.

@en

P1476

Inflammation in Lafora Disease ...... Malin Knock-out Mouse Models.

@en

P2093

Irene López-González

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Isidre Ferrer

http://www.w3.org/2001/XMLSchema#string

Pascual Sanz

http://www.w3.org/2001/XMLSchema#string

P2860

Malin decreases glycogen accumulation by promoting the degradation of protein targeting to glycogen (PTG)

Laforin, the most common protein mutated in Lafora disease, regulates autophagy

Laforin is required for the functional activation of malin in endoplasmic reticulum stress resistance in neuronal cells

Autophagy, mitochondria and oxidative stress: cross-talk and redox signalling

Genetic and Transcriptomic Profiles of Inflammation in Neurodegenerative Diseases: Alzheimer, Parkinson, Creutzfeldt-Jakob and Tauopathies

Laforin, a dual specificity phosphatase that dephosphorylates complex carbohydrates

Oxidative stress, redox signaling, and autophagy: cell death versus survival

Targeted disruption of the Epm2a gene causes formation of Lafora inclusion bodies, neurodegeneration, ataxia, myoclonus epilepsy and impaired behavioral response in mice

A unique carbohydrate binding domain targets the lafora disease phosphatase to glycogen.

Laforin is a glycogen phosphatase, deficiency of which leads to elevated phosphorylation of glycogen in vivo.

P2888

s12035-016-9884-4

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3119-3130

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scholarly article

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10.1007/S12035-016-9884-4

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Rosa Viana

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2016-04-04T00:00:00Z

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1026228473

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27041370

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Inflammation in Lafora Disease: Evolution with Disease Progression in Laforin and Malin Knock-out Mouse Models.

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P2860

P2860

Inflammation in Lafora Disease: Evolution with Disease Progression in Laforin and Malin Knock-out Mouse Models.

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prefLabel

P1433

P1476

P2093

P2860

P2888

P304

P31

P356

P433

P478

P50

P577

P6179

P698

P932

P356

P1433

P1476

P2093

P2860

P2888

P304

P31

P356

P433

P478

P50

P577

P6179

P698

P932