The muscle dystrophy-causing ΔK32 lamin A/C mutant does not impair the functions of the nucleoplasmic lamin-A/C-LAP2α complex in mice.
about
Proliferation of progeria cells is enhanced by lamina-associated polypeptide 2α (LAP2α) through expression of extracellular matrix proteinsThe expression of Lamin A mutant R321X leads to endoplasmic reticulum stress with aberrant Ca2+ handling.Advances in basic and clinical research in laminopathies.Lamins in the nuclear interior - life outside the lamina.Nucleoplasmic lamins define growth-regulating functions of lamina-associated polypeptide 2α in progeria cells.Gene Therapy via Trans-Splicing for LMNA-Related Congenital Muscular Dystrophy.Modeling Skeletal Muscle Laminopathies Using Human Induced Pluripotent Stem Cells Carrying Pathogenic MutationsThe Pathogenesis and Therapies of Striated Muscle Laminopathies
P2860
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P2860
The muscle dystrophy-causing ΔK32 lamin A/C mutant does not impair the functions of the nucleoplasmic lamin-A/C-LAP2α complex in mice.
description
2013 nî lūn-bûn
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2013年の論文
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2013年論文
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2013年論文
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2013年論文
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2013年論文
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2013年論文
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2013年论文
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2013年论文
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2013年论文
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name
The muscle dystrophy-causing Δ ...... min-A/C-LAP2α complex in mice.
@en
The muscle dystrophy-causing Δ ...... min-A/C-LAP2α complex in mice.
@nl
type
label
The muscle dystrophy-causing Δ ...... min-A/C-LAP2α complex in mice.
@en
The muscle dystrophy-causing Δ ...... min-A/C-LAP2α complex in mice.
@nl
prefLabel
The muscle dystrophy-causing Δ ...... min-A/C-LAP2α complex in mice.
@en
The muscle dystrophy-causing Δ ...... min-A/C-LAP2α complex in mice.
@nl
P2093
P2860
P356
P1476
The muscle dystrophy-causing Δ ...... min-A/C-LAP2α complex in mice.
@en
P2093
Anne T Bertrand
Gisèle Bonne
Ivana Gotic
Katarzyna Biadasiewicz
Nikola Woisetschläger
Rita Spilka
Thomas Dechat
Ursula Pilat
P2860
P304
P356
10.1242/JCS.115246
P407
P577
2013-02-26T00:00:00Z