The human mitochondrial ISCA1, ISCA2, and IBA57 proteins are required for [4Fe-4S] protein maturation. - Wikidata - wikimedia - TriplyDB

The human mitochondrial ISCA1, ISCA2, and IBA57 proteins are required for [4Fe-4S] protein maturation.

The human mitochondrial ISCA1, ISCA2, and IBA57 proteins are required for [4Fe-4S] protein maturation.

http://www.wikidata.org/entity/Q42072342

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Iron-sulfur cluster biogenesis in mammalian cells: New insights into the molecular mechanisms of cluster delivery The role of mitochondria in cellular iron-sulfur protein biogenesis: mechanisms, connected processes, and diseases [2Fe-2S] cluster transfer in iron-sulfur protein biogenesis Functional reconstitution of mitochondrial Fe/S cluster synthesis on Isu1 reveals the involvement of ferredoxin Mitochondrial Bol1 and Bol3 function as assembly factors for specific iron-sulfur proteins.Role of Nfu1 and Bol3 in iron-sulfur cluster transfer to mitochondrial clients.ISCA1 is essential for mitochondrial Fe4S4 biogenesis in vivo.Copper binding in IscA inhibits iron-sulphur cluster assembly in Escherichia coli.The diabetes drug target MitoNEET governs a novel trafficking pathway to rebuild an Fe-S cluster into cytosolic aconitase/iron regulatory protein 1 Malfunctioning of the iron-sulfur cluster assembly machinery in Saccharomyces cerevisiae produces oxidative stress via an iron-dependent mechanism, causing dysfunction in respiratory complexes.Deletion of the Proposed Iron Chaperones IscA/SufA Results in Accumulation of a Red Intermediate Cysteine Desulfurase IscS in Escherichia coli.iTRAQ-Based Quantitative Proteomics Identifies Potential Regulatory Proteins Involved in Chicken Eggshell Brownness.Protein-mediated assembly of succinate dehydrogenase and its cofactors Loss of cardiolipin leads to perturbation of mitochondrial and cellular iron homeostasis Spectroscopic and functional characterization of iron-sulfur cluster-bound forms of Azotobacter vinelandii (Nif)IscA.Superoxide triggers an acid burst in Saccharomyces cerevisiae to condition the environment of glucose-starved cells The iron-sulfur cluster assembly machineries in plants: current knowledge and open questions.Structural/Functional Properties of Human NFU1, an Intermediate [4Fe-4S] Carrier in Human Mitochondrial Iron-Sulfur Cluster Biogenesis.Mammalian Fe-S proteins: definition of a consensus motif recognized by the co-chaperone HSC20 Aconitase post-translational modification as a key in linkage between Krebs cycle, iron homeostasis, redox signaling, and metabolism of reactive oxygen species.The spectrum of pyruvate oxidation defects in the diagnosis of mitochondrial disorders.Mitochondrial iron-sulfur cluster biogenesis from molecular understanding to clinical disease.Mutation of the iron-sulfur cluster assembly gene IBA57 causes fatal infantile leukodystrophy.Mitochondria and Iron: current questions.Iron-sulfur cluster biogenesis and trafficking in mitochondria.CISD1 in association with obesity-associated dysfunctional adipogenesis in human visceral adipose tissue.Genome-wide association study on antipsychotic-induced weight gain in the CATIE sample.Evolutionary conservation and in vitro reconstitution of microsporidian iron-sulfur cluster biosynthesis.IBA57 mutations abrogate iron-sulfur cluster assembly leading to cavitating leukoencephalopathy.ISCA2 mutation causes infantile neurodegenerative mitochondrial disorder.Homozygous p.(Glu87Lys) variant in ISCA1 is associated with a multiple mitochondrial dysfunctions syndrome.Evidence for a catalytically and kinetically competent enzyme-substrate cross-linked intermediate in catalysis by lipoyl synthase Mutation of the iron-sulfur cluster assembly gene IBA57 causes severe myopathy and encephalopathy.The mitochondrial Hsp70 chaperone Ssq1 facilitates Fe/S cluster transfer from Isu1 to Grx5 by complex formation.Spectroscopic and functional characterization of iron-bound forms of Azotobacter vinelandii (Nif)IscA.Protein expression profiles in patients carrying NFU1 mutations. Contribution to the pathophysiology of the disease.In vitro characterization of a novel Isu homologue from Drosophila melanogaster for de novo FeS-cluster formation.Genes for iron metabolism influence circadian rhythms in Drosophila melanogaster.A novel de novo dominant mutation in ISCU associated with mitochondrial myopathy.Iron-sulfur cluster biosynthesis and trafficking - impact on human disease conditions.

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The human mitochondrial ISCA1, ISCA2, and IBA57 proteins are required for [4Fe-4S] protein maturation.

http://www.wikidata.org/entity/Q42072342

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2012 nî lūn-bûn

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2012年の論文

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2012年学术文章

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2012年學術文章

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The human mitochondrial ISCA1, ...... r [4Fe-4S] protein maturation.

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The human mitochondrial ISCA1, ...... r [4Fe-4S] protein maturation.

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type

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The human mitochondrial ISCA1, ...... r [4Fe-4S] protein maturation.

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The human mitochondrial ISCA1, ...... r [4Fe-4S] protein maturation.

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The human mitochondrial ISCA1, ...... r [4Fe-4S] protein maturation.

@en

The human mitochondrial ISCA1, ...... r [4Fe-4S] protein maturation.

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MBC.E11-09-0772

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Molecular Biology of the Cell

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The human mitochondrial ISCA1, ...... r [4Fe-4S] protein maturation.

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P2093

Alex D Sheftel

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Brigitte Niggemeyer

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Claudia Wilbrecht

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Hans-Peter Elsässer

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Oliver Stehling

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Ulrich Mühlenhoff

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P2860

Characterization of the human HSC20, an unusual DnaJ type III protein, involved in iron-sulfur cluster biogenesis

Role of human mitochondrial Nfs1 in cytosolic iron-sulfur protein biogenesis and iron regulation

Glutaredoxin 5 deficiency causes sideroblastic anemia by specifically impairing heme biosynthesis and depleting cytosolic iron in human erythroblasts

Iron-sulfur protein maturation in human cells: evidence for a function of frataxin

Human ind1, an iron-sulfur cluster assembly factor for respiratory complex I

Human Nbp35 is essential for both cytosolic iron-sulfur protein assembly and iron homeostasis

Human iron-sulfur cluster assembly, cellular iron homeostasis, and disease

Specialized function of yeast Isa1 and Isa2 proteins in the maturation of mitochondrial [4Fe-4S] proteins.

Isa1p is a component of the mitochondrial machinery for maturation of cellular iron-sulfur proteins and requires conserved cysteine residues for function.

Role of Saccharomyces cerevisiae ISA1 and ISA2 in iron homeostasis

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1157-1166

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10.1091/MBC.E11-09-0772

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3315811

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