Four monoclonal antibodies inhibit the recognition of arylsulphatase A by the lysosomal enzyme phosphotransferase.
about
Function and properties of chimeric MPR 46-MPR 300 mannose 6-phosphate receptorsDefective oligomerization of arylsulfatase a as a cause of its instability in lysosomes and metachromatic leukodystrophyDeveloping therapeutic approaches for metachromatic leukodystrophyRecognition of arylsulfatase A and B by the UDP-N-acetylglucosamine:lysosomal enzyme N-acetylglucosamine-phosphotransferase.Interaction of arylsulfatase A with UDP-N-acetylglucosamine:Lysosomal enzyme-N-acetylglucosamine-1-phosphotransferase.The functional consequences of mis-sense mutations affecting an intra-molecular salt bridge in arylsulphatase A.Saposin B-dependent reconstitution of arylsulfatase A activity in vitro and in cell culture models of metachromatic leukodystrophy.Specific hammerhead ribozymes reduce synthesis of cation-independent mannose 6-phosphate receptor mRNA and protein.Metachromatic leukodystrophy - mutation analysis provides further evidence of genotype-phenotype correlation.
P2860
Q22254028-7866FB5B-B784-4DAF-99BD-3C052C19DA83Q27637145-74407BFD-D8BD-47AA-9384-EB69F1194AACQ28297086-8C7CA991-CB8E-409A-B1DC-EF39C2C22FD3Q40642753-89339757-03C1-4E2F-81D1-6F4E0BD20C86Q40977552-9DE9D467-6AE4-4188-9349-56802D928EEEQ42125367-AA44A361-9738-4AEB-AEA2-29194D2D510CQ43148425-AEA72DA8-6421-4BC8-AE2C-8DD4886FBFE1Q44542544-96451239-35F9-45A4-9E27-55A91FD360A6Q45880285-AC79BB6C-D882-4F82-85BE-B5C4072173E8
P2860
Four monoclonal antibodies inhibit the recognition of arylsulphatase A by the lysosomal enzyme phosphotransferase.
description
1994 nî lūn-bûn
@nan
1994年の論文
@ja
1994年論文
@yue
1994年論文
@zh-hant
1994年論文
@zh-hk
1994年論文
@zh-mo
1994年論文
@zh-tw
1994年论文
@wuu
1994年论文
@zh
1994年论文
@zh-cn
name
Four monoclonal antibodies inh ...... mal enzyme phosphotransferase.
@en
Four monoclonal antibodies inh ...... mal enzyme phosphotransferase.
@nl
type
label
Four monoclonal antibodies inh ...... mal enzyme phosphotransferase.
@en
Four monoclonal antibodies inh ...... mal enzyme phosphotransferase.
@nl
prefLabel
Four monoclonal antibodies inh ...... mal enzyme phosphotransferase.
@en
Four monoclonal antibodies inh ...... mal enzyme phosphotransferase.
@nl
P2093
P2860
P356
P1433
P1476
Four monoclonal antibodies inh ...... mal enzyme phosphotransferase.
@en
P2093
Gieselmann V
Hille-Rehfeld A
Sommerlade HJ
von Figura K
P2860
P304
P356
10.1042/BJ2970123
P407
P478
297 ( Pt 1)
P577
1994-01-01T00:00:00Z