about
Structural basis for the recognition of a nucleoporin FG repeat by the NTF2-like domain of the TAP/p15 mRNA nuclear export factorA novel mode of RBD-protein recognition in the Y14-Mago complexMutation of ribosomal protein RPS24 in Diamond-Blackfan anemia results in a ribosome biogenesis disorderThe structure of the CstF-77 homodimer provides insights into CstF assemblyMolecular basis of Diamond Blackfan anemia: structure and function analysis of RPS19Hexameric architecture of CstF supported by CstF-50 homodimerization domain structureStructure-function analysis of hRPC62 provides insights into RNA polymerase III transcription initiationLocked tether formation by cooperative folding of Rna14p monkeytail and Rna15p hinge domains in the yeast CF IA complexCrucial role of the Rcl1p-Bms1p interaction for yeast pre-ribosomal RNA processingStructural basis for ATP loss by Clp1p in a G135R mutant proteinStructural analysis of human RPC32β-RPC62 complexMutations in the XPD helicase gene result in XP and TTD phenotypes, preventing interaction between XPD and the p44 subunit of TFIIHMolecular structure of human TFIIHClinical spectrum of 4H leukodystrophy caused by POLR3A and POLR3B mutations.Recessive mutations in POLR3B, encoding the second largest subunit of Pol III, cause a rare hypomyelinating leukodystrophy.An essential role for Clp1 in assembly of polyadenylation complex CF IA and Pol II transcription termination.Recessive mutations in POLR1C cause a leukodystrophy by impairing biogenesis of RNA polymerase III.Mutations in the amino-terminal domain of the human poly(ADP-ribose) polymerase that affect its catalytic activity but not its DNA binding capacity.Peptides derived from the bifunctional kinase/RNase enzyme IRE1α modulate IRE1α activity and protect cells from endoplasmic reticulum stress.Sqt1p is an eight-bladed WD40 protein.Chemical shift assignments of a new folded domain from yeast Pcf11.Pwp2 mediates UTP-B assembly via two structurally independent domains.Mutations of POLR3A Encoding a Catalytic Subunit of RNA Polymerase Pol III Cause a Recessive Hypomyelinating Leukodystrophy p415.[Diamond-Blackfan anemia reveals the dark side of ribosome biogenesis].Solution structure of the C-terminal domain of TFIIH P44 subunit reveals a novel type of C4C4 ring domain involved in protein-protein interactions.Deciphering correct strategies for multiprotein complex assembly by co-expression: application to complexes as large as the histone octamer.Structural and functional aspects of winged-helix domains at the core of transcription initiation complexes.The Npa1p complex chaperones the assembly of the earliest eukaryotic large ribosomal subunit precursorStructural and interaction analysis of the Rrp5 C-terminal regionPoly(ADP-ribose) polymerase: structure-function relationshipDissecting the interaction network of multiprotein complexes by pairwise coexpression of subunits in E. coliStructural characterization of the cysteine-rich domain of TFIIH p44 subunitClinical spectrum of POLR3-related leukodystrophy caused by biallelic POLR1C pathogenic variantsThe hRPC62 subunit of human RNA polymerase III displays helicase activityDomain definition and interaction mapping for the endonuclease complex hNob1/hPno1In vitro dimerization of human RIO2 kinaseStructural insights into the 3'-end mRNA maturation machinery: Snapshot on polyadenylation signal recognition
P50
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P50
description
hulumtues
@sq
researcher
@en
wetenschapper
@nl
հետազոտող
@hy
name
Sébastien Fribourg
@ast
Sébastien Fribourg
@en
Sébastien Fribourg
@es
Sébastien Fribourg
@nl
Sébastien Fribourg
@sl
type
label
Sébastien Fribourg
@ast
Sébastien Fribourg
@en
Sébastien Fribourg
@es
Sébastien Fribourg
@nl
Sébastien Fribourg
@sl
prefLabel
Sébastien Fribourg
@ast
Sébastien Fribourg
@en
Sébastien Fribourg
@es
Sébastien Fribourg
@nl
Sébastien Fribourg
@sl
P1053
M-7418-2014
P106
P21
P2798
P31
P3829
P496
0000-0003-4112-7510