Increased longevity and metabolic correction following syngeneic BMT in a murine model of mucopolysaccharidosis type I.

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Effects of enzyme replacement therapy started late in a murine model of mucopolysaccharidosis type I Evidence of a progressive motor dysfunction in Mucopolysaccharidosis type I mice.Standardization of α-L-iduronidase enzyme assay with Michaelis-Menten kinetics.

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Increased longevity and metabolic correction following syngeneic BMT in a murine model of mucopolysaccharidosis type I.

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2011 nî lūn-bûn

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2011年の論文

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2011年論文

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2011年論文

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2011年论文

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name

Increased longevity and metabo ...... mucopolysaccharidosis type I.

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Increased longevity and metabo ...... mucopolysaccharidosis type I.

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Increased longevity and metabo ...... mucopolysaccharidosis type I.

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Increased longevity and metabo ...... mucopolysaccharidosis type I.

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Increased longevity and metabo ...... mucopolysaccharidosis type I.

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Increased longevity and metabo ...... mucopolysaccharidosis type I.

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Increased longevity and metabo ...... mucopolysaccharidosis type I.

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A W Lenander

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C B Whitley

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D A Wolf

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E A Braunlin

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K M Podetz-Pedersen

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P2860

Neurogenesis in the dentate gyrus of the adult rat: age-related decrease of neuronal progenitor proliferation

Murine mucopolysaccharidosis type I: targeted disruption of the murine alpha-L-iduronidase gene

Identification of mutations in the alpha-L-iduronidase gene (IDUA) that cause Hurler and Scheie syndromes

Gene therapy augments the efficacy of hematopoietic cell transplantation and fully corrects mucopolysaccharidosis type I phenotype in the mouse model.

Cord-blood transplants from unrelated donors in patients with Hurler's syndrome.

Long-term effects of bone marrow transplantation in dogs with mucopolysaccharidosis I.

Characterization of an immunodeficient mouse model of mucopolysaccharidosis type I suitable for preclinical testing of human stem cell and gene therapy.

Activated microglia in cortex of mouse models of mucopolysaccharidoses I and IIIB

Direct gene transfer to the CNS prevents emergence of neurologic disease in a murine model of mucopolysaccharidosis type I.

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bmt.2011.239

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1235-1240

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scholarly article

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10.1038/BMT.2011.239

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English

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Increased longevity and metabolic correction following syngeneic BMT in a murine model of mucopolysaccharidosis type I.

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P2860

P2860

Increased longevity and metabolic correction following syngeneic BMT in a murine model of mucopolysaccharidosis type I.

description

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P1476

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