Solution structure of the transforming growth factor beta-binding protein-like module, a domain associated with matrix fibrils
about
The evolution of extracellular fibrillins and their functional domainsSpecific sequence motif of 8-Cys repeats of TGF-beta binding proteins, LTBPs, creates a hydrophobic interaction surface for binding of small latent TGF-betaStructure of the integrin binding fragment from fibrillin-1 gives new insights into microfibril organizationThe latent transforming growth factor beta binding protein (LTBP) familyStructure and interdomain interactions of a hybrid domain: a disulphide-rich module of the fibrillin/LTBP superfamily of matrix proteinsThe molecular genetics of Marfan syndrome and related disordersFibrillin: from microfibril assembly to biomechanical functionThe molecular genetics of Marfan syndrome and related microfibrillopathiesRETRACTED: TGFβ1 signaling via αVβ6 integrinAbsence of autoantibodies against correctly folded recombinant fibrillin-1 protein in systemic sclerosis patientsStructure of the Fibrillin-1 N-Terminal Domains Suggests that Heparan Sulfate Regulates the Early Stages of Microfibril AssemblyTargeting of bone morphogenetic protein growth factor complexes to fibrillinCell adhesion to fibrillin-1 molecules and microfibrils is mediated by alpha 5 beta 1 and alpha v beta 3 integrinsTen novel FBN2 mutations in congenital contractural arachnodactyly: delineation of the molecular pathogenesis and clinical phenotypeEffects of proline cis-trans isomerization on TB domain secondary structure.Coherent multidimensional vibrational spectroscopy of biomolecules: concepts, simulations, and challenges.Dissecting coherent vibrational spectra of small proteins into secondary structural elements by sensitivity analysisMutations in fibrillin-1 cause congenital scleroderma: stiff skin syndrome.Fibrillin-1 interactions with fibulins depend on the first hybrid domain and provide an adaptor function to tropoelastin.Marfan syndrome in the third Millennium.Nanostructure of fibrillin-1 reveals compact conformation of EGF arrays and mechanism for extensibility.Mutations in the TGFβ binding-protein-like domain 5 of FBN1 are responsible for acromicric and geleophysic dysplasias.A new novel mutation in FBN1 causes autosomal dominant Marfan syndrome in a Chinese family.Fibrillin-containing microfibrils are key signal relay stations for cell function.Two novel FBN1 mutations associated with ectopia lentis and marfanoid habitus in two Chinese familiesMolecular pathogenesis and management strategies of ectopia lentis.The pathogenesis of aortopathy in Marfan syndrome and related diseases.TB domain proteins: evolutionary insights into the multifaceted roles of fibrillins and LTBPs.¹H, ¹³C and ¹⁵N assignments of the four N-terminal domains of human fibrillin-1.Classical and neonatal Marfan syndrome mutations in fibrillin-1 cause differential protease susceptibilities and protein function.A microfibril assembly assay identifies different mechanisms of dominance underlying Marfan syndrome, stiff skin syndrome and acromelic dysplasiasNMR spectroscopic and bioinformatic analyses of the LTBP1 C-terminus reveal a highly dynamic domain organisation.The supramolecular organization of fibrillin-rich microfibrils.Editorial Commentary: Understanding Marfan syndrome, or "how not to invent the light bulb".Modification of the structure and function of fibrillin-1 by homocysteine suggests a potential pathogenetic mechanism in homocystinuria.Arg-Gly-Asp-containing domains of fibrillins-1 and -2 distinctly regulate lung fibroblast migration.LTBPs in biology and medicine: LTBP diseases.NMR of modular proteins.TGGE screening of the entire FBN1 coding sequence in 126 individuals with marfan syndrome and related fibrillinopathies.Molecular basis of elastic fiber formation. Critical interactions and a tropoelastin-fibrillin-1 cross-link.
P2860
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P2860
Solution structure of the transforming growth factor beta-binding protein-like module, a domain associated with matrix fibrils
description
1997 nî lūn-bûn
@nan
1997年の論文
@ja
1997年論文
@yue
1997年論文
@zh-hant
1997年論文
@zh-hk
1997年論文
@zh-mo
1997年論文
@zh-tw
1997年论文
@wuu
1997年论文
@zh
1997年论文
@zh-cn
name
Solution structure of the tran ...... associated with matrix fibrils
@en
Solution structure of the tran ...... associated with matrix fibrils
@nl
type
label
Solution structure of the tran ...... associated with matrix fibrils
@en
Solution structure of the tran ...... associated with matrix fibrils
@nl
prefLabel
Solution structure of the tran ...... associated with matrix fibrils
@en
Solution structure of the tran ...... associated with matrix fibrils
@nl
P2093
P2860
P356
P1433
P1476
Solution structure of the tran ...... associated with matrix fibrils
@en
P2093
P2860
P304
P356
10.1093/EMBOJ/16.22.6659
P407
P577
1997-11-01T00:00:00Z