The chondrodystrophy, nanomelia: biosynthesis and processing of the defective aggrecan precursor.
about
The aggrecanopathies; an evolving phenotypic spectrum of human genetic skeletal diseasesMolecular cloning and functional expression of the rat 175-kDa hyaluronan receptor for endocytosisThe C-type lectin of the aggrecan G3 domain activates complement.Molecular dissection of craniofacial development using zebrafish.Regulation of chondrocyte differentiation by the actin cytoskeleton and adhesive interactions.Accumulation of a pentasaccharide terminating in alpha-N-acetylglucosamine in an animal cell mutant defective in heparan sulfate biosynthesis.Aggrecan is expressed by embryonic brain glia and regulates astrocyte development.Role of the C-terminal G3 domain in sorting and secretion of aggrecan core protein and ubiquitin-mediated degradation of accumulated mutant precursors.Roles of aggrecan domains in biosynthesis, modification by glycosaminoglycans and product secretion.Aggrecan is required for growth plate cytoarchitecture and differentiation.The biochemical characterization of aggrecan from normal and tibial-dyschondroplastic chicken growth-plate cartilage.The folded modules of aggrecan G3 domain exert two separable functions in glycosaminoglycan modification and product secretion.Bulldog dwarfism in Dexter cattle is caused by mutations in ACAN.
P2860
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P2860
The chondrodystrophy, nanomelia: biosynthesis and processing of the defective aggrecan precursor.
description
1994 nî lūn-bûn
@nan
1994年の論文
@ja
1994年論文
@yue
1994年論文
@zh-hant
1994年論文
@zh-hk
1994年論文
@zh-mo
1994年論文
@zh-tw
1994年论文
@wuu
1994年论文
@zh
1994年论文
@zh-cn
name
The chondrodystrophy, nanomeli ...... defective aggrecan precursor.
@en
The chondrodystrophy, nanomeli ...... defective aggrecan precursor.
@nl
type
label
The chondrodystrophy, nanomeli ...... defective aggrecan precursor.
@en
The chondrodystrophy, nanomeli ...... defective aggrecan precursor.
@nl
prefLabel
The chondrodystrophy, nanomeli ...... defective aggrecan precursor.
@en
The chondrodystrophy, nanomeli ...... defective aggrecan precursor.
@nl
P2093
P2860
P356
P1433
P1476
The chondrodystrophy, nanomeli ...... defective aggrecan precursor.
@en
P2093
P2860
P304
P356
10.1042/BJ3010211
P407
P478
301 ( Pt 1)
P577
1994-07-01T00:00:00Z