Circadian rhythm and suprachiasmatic nucleus alterations in the mouse model of mucopolysaccharidosis IIIB.
about
Female mucopolysaccharidosis IIIA mice exhibit hyperactivity and a reduced sense of danger in the open field testHematopoietic stem cell and gene therapy corrects primary neuropathology and behavior in mucopolysaccharidosis IIIA mice.Myeloid/Microglial driven autologous hematopoietic stem cell gene therapy corrects a neuronopathic lysosomal diseaseBrain RNA-Seq Profiling of the Mucopolysaccharidosis Type II Mouse Model.Genistein improves neuropathology and corrects behaviour in a mouse model of neurodegenerative metabolic diseaseDefects in the medial entorhinal cortex and dentate gyrus in the mouse model of Sanfilippo syndrome type B.Neuropathology in mouse models of mucopolysaccharidosis type I, IIIA and IIIBHeparin cofactor II-thrombin complex and dermatan sulphate:chondroitin sulphate ratio are biomarkers of short- and long-term treatment effects in mucopolysaccharide diseasesAssessment of sleep in children with mucopolysaccharidosis type III.Actigraphic investigation of circadian rhythm functioning and activity levels in children with mucopolysaccharidosis type III (Sanfilippo syndrome)Identification of age-dependent motor and neuropsychological behavioural abnormalities in a mouse model of Mucopolysaccharidosis Type IIBusulfan conditioning enhances engraftment of hematopoietic donor-derived cells in the brain compared with irradiation.Sleep Disorders in Childhood Neurogenetic Disorders.Circadian profiling in two mouse models of lysosomal storage disorders; Niemann Pick type-C and Sandhoff disease.Biochemical, histological and functional correction of mucopolysaccharidosis type IIIB by intra-cerebrospinal fluid gene therapy.Hyperactive behaviour in the mouse model of mucopolysaccharidosis IIIB in the open field and home cage environments.A novel adeno-associated virus capsid with enhanced neurotropism corrects a lysosomal transmembrane enzyme deficiency.
P2860
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P2860
Circadian rhythm and suprachiasmatic nucleus alterations in the mouse model of mucopolysaccharidosis IIIB.
description
2010 nî lūn-bûn
@nan
2010年の論文
@ja
2010年学术文章
@wuu
2010年学术文章
@zh
2010年学术文章
@zh-cn
2010年学术文章
@zh-hans
2010年学术文章
@zh-my
2010年学术文章
@zh-sg
2010年學術文章
@yue
2010年學術文章
@zh-hant
name
Circadian rhythm and suprachia ...... of mucopolysaccharidosis IIIB.
@en
Circadian rhythm and suprachia ...... of mucopolysaccharidosis IIIB.
@nl
type
label
Circadian rhythm and suprachia ...... of mucopolysaccharidosis IIIB.
@en
Circadian rhythm and suprachia ...... of mucopolysaccharidosis IIIB.
@nl
prefLabel
Circadian rhythm and suprachia ...... of mucopolysaccharidosis IIIB.
@en
Circadian rhythm and suprachia ...... of mucopolysaccharidosis IIIB.
@nl
P2093
P50
P1476
Circadian rhythm and suprachia ...... of mucopolysaccharidosis IIIB
@en
P2093
Fiona L Wilkinson
J Ed Wraith
Maria M Canal
P304
P356
10.1016/J.BBR.2010.01.045
P407
P577
2010-02-04T00:00:00Z