Ceroid-lipofuscinosis (Batten's disease): pathogenesis and sequential neuropathological changes in the ovine model.
about
Accumulation of the adenosine triphosphate synthase subunit C in the mnd mutant mouse. A model for neuronal ceroid lipofuscinosisA murine model of variant late infantile ceroid lipofuscinosis recapitulates behavioral and pathological phenotypes of human diseaseOvine ceroid-lipofuscinosis is a proteolipid proteinosis.Tissue culture loading test with storage granules from animal models of neuronal ceroid-lipofuscinosis (Batten disease): testing their lysosomal degradability by normal and Batten cells.Increased zinc and manganese in parallel with neurodegeneration, synaptic protein changes and activation of Akt/GSK3 signaling in ovine CLN6 neuronal ceroid lipofuscinosis.The development and characterisation of complex ovine neuron cultures from fresh and frozen foetal neurons.Genetic disorders of sheep in New Zealand: a review and perspective.Manifestation of neuronal ceroid lipofuscinosis in Australian Merino sheep: observations on altered behaviour and growth.Biometals in rare neurodegenerative disorders of childhood.Location and connectivity determine GABAergic interneuron survival in the brains of South Hampshire sheep with CLN6 neuronal ceroid lipofuscinosisAnalysis of NCL Proteins from an Evolutionary Standpoint.The proteasome and the degradation of oxidized proteins: Part II - protein oxidation and proteasomal degradation.The sequence of the major protein stored in ovine ceroid lipofuscinosis is identical with that of the dicyclohexylcarbodiimide-reactive proteolipid of mitochondrial ATP synthase.Lysosomal storage diseases of animals: an essay in comparative pathology.Characterization of the expressed genes for subunit c of mitochondrial ATP synthase in sheep with ceroid lipofuscinosisEnhanced expression of manganese-dependent superoxide dismutase in human and sheep CLN6 tissuesAdult dementia due to intraneuronal accumulation of ceroidlipofuscinosis (Kufs' disease): ultrastructural study of two cases.Neuronal ceroid-lipofuscinosis in Borderdale sheep.Juvenile-onset neuronal ceroid-lipofuscinosis in Rambouillet sheep.Computed tomography provides enhanced techniques for longitudinal monitoring of progressive intracranial volume loss associated with regional neurodegeneration in ovine neuronal ceroid lipofuscinoses
P2860
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P2860
Ceroid-lipofuscinosis (Batten's disease): pathogenesis and sequential neuropathological changes in the ovine model.
description
1989 nî lūn-bûn
@nan
1989年の論文
@ja
1989年学术文章
@wuu
1989年学术文章
@zh-cn
1989年学术文章
@zh-hans
1989年学术文章
@zh-my
1989年学术文章
@zh-sg
1989年學術文章
@yue
1989年學術文章
@zh
1989年學術文章
@zh-hant
name
Ceroid-lipofuscinosis (Batten' ...... al changes in the ovine model.
@en
type
label
Ceroid-lipofuscinosis (Batten' ...... al changes in the ovine model.
@en
prefLabel
Ceroid-lipofuscinosis (Batten' ...... al changes in the ovine model.
@en
P2093
P1476
Ceroid-lipofuscinosis (Batten' ...... al changes in the ovine model.
@en
P2093
P2860
P304
P356
10.1111/J.1365-2990.1989.TB01236.X
P577
1989-07-01T00:00:00Z