Benzo(c)quinolizinium drugs inhibit degradation of Delta F508-CFTR cytoplasmic domain.
about
Emerging novel concept of chaperone therapies for protein misfolding diseasesThe delicate balance between secreted protein folding and endoplasmic reticulum-associated degradation in human physiologyEnhancing the Potency of F508del Correction: A Multi-Layer Combinational Approach to Drug Discovery for Cystic Fibrosis.Pharmacological Correctors of Mutant CFTR Mistrafficking.Sildenafil (Viagra) corrects DeltaF508-CFTR location in nasal epithelial cells from patients with cystic fibrosis.Pharmacological approaches to correcting the ion transport defect in cystic fibrosis.CFTR mutations altering CFTR fragmentation.Pharmacological chaperones for enzyme enhancement therapy in genetic diseases.Pharmacological treatment of the basic defect in cystic fibrosis.Role of calpain in the regulation of CFTR (cystic fibrosis transmembrane conductance regulator) turnover.C terminus of nucleotide binding domain 1 contains critical features for cystic fibrosis transmembrane conductance regulator trafficking and activation.Activation mechanisms for the cystic fibrosis transmembrane conductance regulator protein involve direct binding of cAMP
P2860
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P2860
Benzo(c)quinolizinium drugs inhibit degradation of Delta F508-CFTR cytoplasmic domain.
description
2003 nî lūn-bûn
@nan
2003年の論文
@ja
2003年学术文章
@wuu
2003年学术文章
@zh-cn
2003年学术文章
@zh-hans
2003年学术文章
@zh-my
2003年学术文章
@zh-sg
2003年學術文章
@yue
2003年學術文章
@zh
2003年學術文章
@zh-hant
name
Benzo(c)quinolizinium drugs inhibit degradation of Delta F508-CFTR cytoplasmic domain.
@en
type
label
Benzo(c)quinolizinium drugs inhibit degradation of Delta F508-CFTR cytoplasmic domain.
@en
prefLabel
Benzo(c)quinolizinium drugs inhibit degradation of Delta F508-CFTR cytoplasmic domain.
@en
P2093
P1476
Benzo(c)quinolizinium drugs inhibit degradation of Delta F508-CFTR cytoplasmic domain
@en
P2093
Fiona L L Stratford
Malcolm M C Pereira
Margaret A McPherson
Robert L Dormer
P304
P356
10.1016/S0006-291X(02)02883-8
P407
P50
P577
2003-01-01T00:00:00Z