Further studies on the substrate spectrum of phytanoyl-CoA hydroxylase: implications for Refsum disease?
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Breakdown of 2-hydroxylated straight chain fatty acids via peroxisomal 2-hydroxyphytanoyl-CoA lyase: a revised pathway for the alpha-oxidation of straight chain fatty acidsNormal fur development and sebum production depends on fatty acid 2-hydroxylase expression in sebaceous glandsFatty acid 2-hydroxylase mediates diffusional mobility of Raft-associated lipids, GLUT4 level, and lipogenesis in 3T3-L1 adipocytes.Biochemistry and genetics of inherited disorders of peroxisomal fatty acid metabolismAcyl-CoA thioesterase 9 (ACOT9) in mouse may provide a novel link between fatty acid and amino acid metabolism in mitochondria.Alpha-methylacyl-CoA racemase--an 'obscure' metabolic enzyme takes centre stage.Additional oxidized and alkyl chain breakdown metabolites of the plasticizer DINCH in urine after oral dosage to human volunteers.Disruption of mitochondrial homeostasis by phytanic acid in cerebellum of young rats.Studies on the specificity of unprocessed and mature forms of phytanoyl-CoA 2-hydroxylase and mutation of the iron binding ligands.Marked inhibition of Na+, K(+)- ATPase activity and the respiratory chain by phytanic acid in cerebellum from young rats: possible underlying mechanisms of cerebellar ataxia in Refsum disease.
P2860
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P2860
Further studies on the substrate spectrum of phytanoyl-CoA hydroxylase: implications for Refsum disease?
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2003 nî lūn-bûn
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2003年の論文
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2003年学术文章
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2003年学术文章
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2003年学术文章
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2003年学术文章
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2003年学术文章
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name
Further studies on the substra ...... plications for Refsum disease?
@en
Further studies on the substra ...... plications for Refsum disease?
@nl
type
label
Further studies on the substra ...... plications for Refsum disease?
@en
Further studies on the substra ...... plications for Refsum disease?
@nl
prefLabel
Further studies on the substra ...... plications for Refsum disease?
@en
Further studies on the substra ...... plications for Refsum disease?
@nl
P2093
P2860
P921
P1476
Further studies on the substra ...... plications for Refsum disease?
@en
P2093
Guy P Mannaerts
Paul P Van Veldhoven
Stanny Asselberghs
Veerle Foulon
Wendy Geens
P2860
P304
P356
10.1194/JLR.M300230-JLR200
P577
2003-08-16T00:00:00Z