The Refsum disease marker phytanic acid, a branched chain fatty acid, affects Ca2+ homeostasis and mitochondria, and reduces cell viability in rat hippocampal astrocytes.
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Midlife diagnosis of Refsum disease in siblings with retinitis pigmentosa -- the footprint is the clue: a case reportBrain Lipotoxicity of Phytanic Acid and Very Long-chain Fatty Acids. Harmful Cellular/Mitochondrial Activities in Refsum Disease and X-Linked AdrenoleukodystrophyWhy does brain metabolism not favor burning of fatty acids to provide energy? Reflections on disadvantages of the use of free fatty acids as fuel for brainAutosomal recessive cerebellar ataxias.Biochemistry and genetics of inherited disorders of peroxisomal fatty acid metabolismBrain pyruvate and 2-oxoglutarate dehydrogenase complexes are mitochondrial targets of the CoA ester of the Refsum disease marker phytanic acid.Ataxia with loss of Purkinje cells in a mouse model for Refsum disease.Peroxisomal Disorders: A Review on Cerebellar Pathologies.Phytanic Acid-Induced Neurotoxicological Manifestations and Apoptosis Ameliorated by Mitochondria-Mediated Actions of Melatonin.Alpha-methylacyl-CoA racemase deletion has mutually counteracting effects on T-cell responses, associated with unchanged course of EAE.In brain mitochondria the branched-chain fatty acid phytanic acid impairs energy transduction and sensitizes for permeability transition.Disruption of mitochondrial homeostasis by phytanic acid in cerebellum of young rats.Rotenone-like action of the branched-chain phytanic acid induces oxidative stress in mitochondria.Marked inhibition of Na+, K(+)- ATPase activity and the respiratory chain by phytanic acid in cerebellum from young rats: possible underlying mechanisms of cerebellar ataxia in Refsum disease.Experimental evidence that pristanic acid disrupts mitochondrial homeostasis in brain of young rats.Cell proliferation inhibition and alterations in retinol esterification induced by phytanic acid and docosahexaenoic acid.
P2860
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P2860
The Refsum disease marker phytanic acid, a branched chain fatty acid, affects Ca2+ homeostasis and mitochondria, and reduces cell viability in rat hippocampal astrocytes.
description
2005 nî lūn-bûn
@nan
2005年の論文
@ja
2005年学术文章
@wuu
2005年学术文章
@zh
2005年学术文章
@zh-cn
2005年学术文章
@zh-hans
2005年学术文章
@zh-my
2005年学术文章
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2005年學術文章
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name
The Refsum disease marker phyt ...... in rat hippocampal astrocytes.
@en
The Refsum disease marker phyt ...... in rat hippocampal astrocytes.
@nl
type
label
The Refsum disease marker phyt ...... in rat hippocampal astrocytes.
@en
The Refsum disease marker phyt ...... in rat hippocampal astrocytes.
@nl
prefLabel
The Refsum disease marker phyt ...... in rat hippocampal astrocytes.
@en
The Refsum disease marker phyt ...... in rat hippocampal astrocytes.
@nl
P2093
P921
P1476
The Refsum disease marker phyt ...... in rat hippocampal astrocytes.
@en
P2093
Georg Reiser
Peter Schönfeld
Stefan Kahlert
P304
P356
10.1016/J.NBD.2004.08.010
P577
2005-02-01T00:00:00Z