Production of a severe cystic fibrosis mutation in mice by gene targeting.
about
The genetic advantage hypothesis in cystic fibrosis heterozygotes: a murine studyATP-binding cassette (ABC) transporters in normal and pathological lungEpithelial Anion Transport as Modulator of Chemokine SignalingAnimal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and DivergencesThe small conductance K+ channel, KCNQ1: expression, function, and subunit composition in murine tracheaA functional CFTR assay using primary cystic fibrosis intestinal organoidsPathophysiology of gene-targeted mouse models for cystic fibrosisAssessment of CFTR chloride channel openers in intact normal and cystic fibrosis murine epitheliaCyp1a2(-/-) null mutant mice develop normally but show deficient drug metabolismKCNQ1-dependent transport in renal and gastrointestinal epitheliaBarriers to inhaled gene therapy of obstructive lung diseases: A reviewThe cystic fibrosis transmembrane conductance regulator (CFTR) is expressed in maturation stage ameloblasts, odontoblasts and bone cellsThe switch of intestinal Slc26 exchangers from anion absorptive to HCOFormula secretory mode is dependent on CFTR anion channel function.Impaired cell volume regulation in intestinal crypt epithelia of cystic fibrosis miceChanges of chloride channels in the lacrimal glands of a rabbit model of Sjögren syndrome.Variation in MSRA modifies risk of neonatal intestinal obstruction in cystic fibrosis.CFTR-mediated Cl(-) transport in the acinar and duct cells of rabbit lacrimal gland.Electrolyte transport in the mammalian colon: mechanisms and implications for disease.The mousetrap: what we can learn when the mouse model does not mimic the human disease.Molecular analysis of the ovine cystic fibrosis transmembrane conductance regulator gene.Chloride channels in the kidney: lessons learned from knockout animals.Animal models of gastrointestinal and liver diseases. Animal models of cystic fibrosis: gastrointestinal, pancreatic, and hepatobiliary disease and pathophysiology.Loss of Slc26a9 anion transporter alters intestinal electrolyte and HCO3(-) transport and reduces survival in CFTR-deficient miceCystic fibrosis growth retardation is not correlated with loss of Cftr in the intestinal epithelium.Suppression of CFTR premature termination codons and rescue of CFTR protein and function by the synthetic aminoglycoside NB54Composition of mineralizing incisor enamel in cystic fibrosis transmembrane conductance regulator-deficient mice.Cholic acid induces a Cftr dependent biliary secretion and liver growth response in mice.A mouse model for the delta F508 allele of cystic fibrosis.Restoration of CFTR function in patients with cystic fibrosis carrying the F508del-CFTR mutationIn vivo activation of the cystic fibrosis transmembrane conductance regulator mutant deltaF508 in murine nasal epitheliumPancreatic pathophysiology in cystic fibrosis.Regulation of murine airway surface liquid volume by CFTR and Ca2+-activated Cl- conductancesLentiviral vector gene transfer to porcine airways.Cystic fibrosis mouse models.Comparative biology of cystic fibrosis animal modelsSmall-molecule CFTR activators increase tear secretion and prevent experimental dry eye diseaseWhat have we learned from mouse models for cystic fibrosis?Generation of a conditional null allele for Cftr in mice.Animal models of chronic lung infection with Pseudomonas aeruginosa: useful tools for cystic fibrosis studies.Knockout mouse models for intestinal electrolyte transporters and regulatory PDZ adaptors: new insights into cystic fibrosis, secretory diarrhoea and fructose-induced hypertension.
P2860
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P2860
Production of a severe cystic fibrosis mutation in mice by gene targeting.
description
1993 nî lūn-bûn
@nan
1993年の論文
@ja
1993年学术文章
@wuu
1993年学术文章
@zh
1993年学术文章
@zh-cn
1993年学术文章
@zh-hans
1993年学术文章
@zh-my
1993年学术文章
@zh-sg
1993年學術文章
@yue
1993年學術文章
@zh-hant
name
Production of a severe cystic fibrosis mutation in mice by gene targeting.
@en
Production of a severe cystic fibrosis mutation in mice by gene targeting.
@nl
type
label
Production of a severe cystic fibrosis mutation in mice by gene targeting.
@en
Production of a severe cystic fibrosis mutation in mice by gene targeting.
@nl
prefLabel
Production of a severe cystic fibrosis mutation in mice by gene targeting.
@en
Production of a severe cystic fibrosis mutation in mice by gene targeting.
@nl
P2093
P2860
P356
P1433
P1476
Production of a severe cystic fibrosis mutation in mice by gene targeting.
@en
P2093
Anderson JR
Cuthbert AW
MacVinish LJ
Ratcliff R
P2860
P2888
P356
10.1038/NG0593-35
P407
P577
1993-05-01T00:00:00Z
P5875
P6179
1014274397