A diet-induced mouse model for glutaric aciduria type I. - Wikidata - wikimedia - TriplyDB

A diet-induced mouse model for glutaric aciduria type I.

A diet-induced mouse model for glutaric aciduria type I.

http://www.wikidata.org/entity/Q46919023

about

Ammonium accumulation and cell death in a rat 3D brain cell model of glutaric aciduria type I Multi-organ abnormalities and mTORC1 activation in zebrafish model of multiple acyl-CoA dehydrogenase deficiency Glutaric acid-mediated apoptosis in primary striatal neurons Increased blood-brain barrier permeability and alterations in perivascular astrocytes and pericytes induced by intracisternal glutaric acid.Cerebral haemodynamics in patients with glutaryl-coenzyme A dehydrogenase deficiency.Mechanistic effects of amino acids and glucose in a novel glutaric aciduria type 1 cell model Effects of targeted suppression of glutaryl-CoA dehydrogenase by lentivirus-mediated shRNA and excessive intake of lysine on apoptosis in rat striatal neurons.Increased glutamate receptor and transporter expression in the cerebral cortex and striatum of gcdh-/- mice: possible implications for the neuropathology of glutaric acidemia type I.Mechanism of age-dependent susceptibility and novel treatment strategy in glutaric acidemia type I Dual mechanism of brain injury and novel treatment strategy in maple syrup urine disease Disruption of mitochondrial homeostasis in organic acidurias: insights from human and animal studies.A role of astrocytes in mediating postnatal neurodegeneration in Glutaric acidemia-type 1.Higher Vulnerability of Menadione-Exposed Cortical Astrocytes of Glutaryl-CoA Dehydrogenase Deficient Mice to Oxidative Stress, Mitochondrial Dysfunction, and Cell Death: Implications for the Neurodegeneration in Glutaric Aciduria Type I.Glutaric aciduria type 1 metabolites impair the succinate transport from astrocytic to neuronal cells Impairment of GABAergic system contributes to epileptogenesis in glutaric acidemia type I.Oxidative Stress, Disrupted Energy Metabolism, and Altered Signaling Pathways in Glutaryl-CoA Dehydrogenase Knockout Mice: Potential Implications of Quinolinic Acid Toxicity in the Neuropathology of Glutaric Acidemia Type I.Mechanism of metabolic stroke and spontaneous cerebral hemorrhage in glutaric aciduria type I.White matter injury induced by perinatal exposure to glutaric acid.Dynamic changes of striatal and extrastriatal abnormalities in glutaric aciduria type I.Induction of Neuroinflammatory Response and Histopathological Alterations Caused by Quinolinic Acid Administration in the Striatum of Glutaryl-CoA Dehydrogenase Deficient Mice.Heparan sulfate mediates neuroprotection from degeneration in experimental glutaric aciduria.Multimodal imaging of striatal degeneration in Amish patients with glutaryl-CoA dehydrogenase deficiency.Striatal neuronal death mediated by astrocytes from the Gcdh-/- mouse model of glutaric acidemia type I.m-Trifluoromethyl diphenyl diselenide attenuates glutaric acid-induced seizures and oxidative stress in rat pups: involvement of the γ-aminobutyric acidergic system.Altered Redox Homeostasis in Branched-Chain Amino Acid Disorders, Organic Acidurias, and Homocystinuria.

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A diet-induced mouse model for glutaric aciduria type I.

http://www.wikidata.org/entity/Q46919023

description

2006 nî lūn-bûn

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2006年の論文

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2006年学术文章

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2006年学术文章

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2006年学术文章

@zh-cn

2006年学术文章

@zh-hans

2006年学术文章

@zh-my

2006年学术文章

@zh-sg

2006年學術文章

@yue

2006年學術文章

@zh-hant

name

A diet-induced mouse model for glutaric aciduria type I.

@en

A diet-induced mouse model for glutaric aciduria type I.

@nl

type

label

A diet-induced mouse model for glutaric aciduria type I.

@en

A diet-induced mouse model for glutaric aciduria type I.

@nl

prefLabel

A diet-induced mouse model for glutaric aciduria type I.

@en

A diet-induced mouse model for glutaric aciduria type I.

@nl

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A diet-induced mouse model for glutaric aciduria type I.

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David A Antonetti

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Ellen B Wolpert

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James R Connor

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Jelena Lazovic

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Keith C Cheng

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Michael B Smith

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Michael Woontner

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Stephen I Goodman

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William J Zinnanti

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899-910

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scholarly article

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10.1093/BRAIN/AWL009

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Pt 4

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129

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2006-01-30T00:00:00Z

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7328193

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16446282

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