DARS2 protects against neuroinflammation and apoptotic neuronal loss, but is dispensable for myelin producing cells.

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Leukoencephalopathy with Brain Stem and Spinal Cord Involvement and not Always Lactate Elevation.

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DARS2 protects against neuroinflammation and apoptotic neuronal loss, but is dispensable for myelin producing cells.

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http://www.wikidata.org/entity/Q47687020

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2017 nî lūn-bûn

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2017年の論文

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2017年学术文章

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2017年学术文章

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2017年学术文章

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2017年学术文章

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2017年学术文章

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2017年學術文章

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2017年學術文章

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2017年學術文章

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name

DARS2 protects against neuroin ...... le for myelin producing cells.

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DARS2 protects against neuroin ...... le for myelin producing cells.

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DARS2 protects against neuroin ...... le for myelin producing cells.

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DARS2 protects against neuroin ...... le for myelin producing cells.

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DARS2 protects against neuroin ...... le for myelin producing cells.

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DARS2 protects against neuroin ...... le for myelin producing cells.

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P1476

DARS2 protects against neuroin ...... ble for myelin producing cells

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Aleksandra Trifunovic

http://www.w3.org/2001/XMLSchema#string

Elena Rugarli

http://www.w3.org/2001/XMLSchema#string

Marijana Aradjanski

http://www.w3.org/2001/XMLSchema#string

Rolf Wibom

http://www.w3.org/2001/XMLSchema#string

Shuaiyu Wang

http://www.w3.org/2001/XMLSchema#string

Steffen Hermans

http://www.w3.org/2001/XMLSchema#string

Stephan Lotter

http://www.w3.org/2001/XMLSchema#string

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MTERF4 regulates translation by targeting the methyltransferase NSUN4 to the mammalian mitochondrial ribosome

Mitochondrial aspartyl-tRNA synthetase deficiency causes leukoencephalopathy with brain stem and spinal cord involvement and lactate elevation

MTERF3 is a negative regulator of mammalian mtDNA transcription

Mitochondrial DNA polymerase gamma is essential for mammalian embryogenesis

A defect in the mitochondrial complex III, but not complex IV, triggers early ROS-dependent damage in defined brain regions.

Cytochrome c oxidase deficiency in neurons decreases both oxidative stress and amyloid formation in a mouse model of Alzheimer's disease

Mice with mitochondrial complex I deficiency develop a fatal encephalomyopathy.

Analysis of Alzheimer's disease severity across brain regions by topological analysis of gene co-expression networks.

Mutations in DARS cause hypomyelination with brain stem and spinal cord involvement and leg spasticity.

Schwann cell mitochondrial metabolism supports long-term axonal survival and peripheral nerve function

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4181-4189

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scholarly article

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10.1093/HMG/DDX307

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http://www.w3.org/2001/XMLSchema#string

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Sukru Anil Dogan

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2017-11-01T00:00:00Z

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28985337

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P921

apoptotic process

neuronitis

DARS2 protects against neuroinflammation and apoptotic neuronal loss, but is dispensable for myelin producing cells.

about

P2860

P2860

DARS2 protects against neuroinflammation and apoptotic neuronal loss, but is dispensable for myelin producing cells.

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