Mechanisms of Sustained Neutrophilia in Patient WHIM-09, Cured of WHIM Syndrome by Chromothripsis.

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Multisystem multitasking by CXCL12 and its receptors CXCR4 and ACKR3.

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Mechanisms of Sustained Neutrophilia in Patient WHIM-09, Cured of WHIM Syndrome by Chromothripsis.

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2017 nî lūn-bûn

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2017年の論文

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2017年学术文章

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2017年学术文章

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2017年学术文章

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2017年学术文章

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2017年學術文章

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name

Mechanisms of Sustained Neutro ...... IM Syndrome by Chromothripsis.

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Mechanisms of Sustained Neutro ...... IM Syndrome by Chromothripsis.

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Mechanisms of Sustained Neutro ...... IM Syndrome by Chromothripsis.

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Mechanisms of Sustained Neutro ...... IM Syndrome by Chromothripsis.

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Mechanisms of Sustained Neutro ...... IM Syndrome by Chromothripsis.

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Mechanisms of Sustained Neutro ...... IM Syndrome by Chromothripsis.

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Mechanisms of Sustained Neutro ...... IM Syndrome by Chromothripsis.

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Alexander Y Yang

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Daniel S Velez

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David H McDermott

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Elena J Cho

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Ji-Liang Gao

http://www.w3.org/2001/XMLSchema#string

Philip M Murphy

http://www.w3.org/2001/XMLSchema#string

Qian Liu

http://www.w3.org/2001/XMLSchema#string

Zhanzhuo Li

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P2860

In vivo two-photon imaging reveals monocyte-dependent neutrophil extravasation during pulmonary inflammation.

Live imaging of neutrophil motility in a zebrafish model of WHIM syndrome

Neutrophil mobilization via plerixafor-mediated CXCR4 inhibition arises from lung demargination and blockade of neutrophil homing to the bone marrow

Hematological findings in the Norrbottnian type of Gaucher disease.

Myelokathexis, a congenital disorder of severe neutropenia characterized by accelerated apoptosis and defective expression of bcl-x in neutrophil precursors.

CXCR2 and CXCR4 antagonistically regulate neutrophil trafficking from murine bone marrow

Mutations in the chemokine receptor gene CXCR4 are associated with WHIM syndrome, a combined immunodeficiency disease.

The CXCR4 antagonist plerixafor is a potential therapy for myelokathexis, WHIM syndrome.

The effect of splenectomy on the leucocyte count.

A new familial immunodeficiency disorder characterized by severe neutropenia, a defective marrow release mechanism, and hypogammaglobulinemia.

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Mechanisms of Sustained Neutrophilia in Patient WHIM-09, Cured of WHIM Syndrome by Chromothripsis.

about

P2860

P2860

Mechanisms of Sustained Neutrophilia in Patient WHIM-09, Cured of WHIM Syndrome by Chromothripsis.

description

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